EHHADH 抗体 (AA 673-723)
Quick Overview for EHHADH 抗体 (AA 673-723) (ABIN7451013)
抗原
See all EHHADH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 673-723
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原理
- Rabbit anti-PBE Antibody, Affinity Purified
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预测反应
- Orangutan
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纯化方法
- Affinity Purified
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免疫原
- between AA 673 and 723
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亚型
- IgG
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应用备注
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IP: 2 - 10 μg/mg lysate
WB: 1:500 - 1:2,500
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限制
- 仅限研究用
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浓度
- 1000 μg/mL
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缓冲液
- Tris-citrate/phosphate buffer, pH 7 to 8 containing 0.09 % Sodium Azide
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- 4 °C
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有效期
- 12 months
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- EHHADH (Enoyl-CoA, Hydratase/3-Hydroxyacyl CoA Dehydrogenase (EHHADH))
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别名
- PBE
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背景
- Background: Peroxisomal bifunctional enzyme (PBE) is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of PBE contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in the PBE gene are a cause of peroxisomal disorders such as Zellweger syndrome [taken from NCBI Entrez Gene (Gene ID: 1962)].
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基因ID
- 1962
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NCBI登录号
- NP_001957
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UniProt
- Q08426
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途径
- Monocarboxylic Acid Catabolic Process
抗原
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