PEX12 抗体 (AA 290-359)
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北京 101111
Quick Overview for PEX12 抗体 (AA 290-359) (ABIN7269246)
抗原
See all PEX12 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 290-359
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原理
- PEX12 Rabbit pAb
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序列
- YNSDSPLLPK MKTVCPLCRK TRVNDTVLAT SGYVFCYRCV FHYVRSHQAC PITGYPTEVQ HLIKLYSPEN
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交叉反应
- 人
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产品特性
- Polyclonal Antibodies
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纯化方法
- Affinity purification
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免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 290-359 of human PEX12 (NP_000277.1).
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亚型
- IgG
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应用备注
- WB,1:500 - 1:2000
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- PEX12 (Peroxisomal Biogenesis Factor 12 (PEX12))
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别名
- PEX12
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背景
- This gene belongs to the peroxin-12 family. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS).,PEX12,PAF-3,PBD3A,Signal Transduction,PEX12
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分子量
- 40kDa
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基因ID
- 5193
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UniProt
- O00623
抗原
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