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GALC 抗体

GALC 适用: 人 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7190741
发货至: 中国
  • 抗原 See all GALC 抗体
    GALC (Galactosylceramidase (GALC))
    适用
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    宿主
    • 32
    • 3
    克隆类型
    • 32
    • 3
    多克隆
    标记
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    This GALC antibody is un-conjugated
    应用范围
    • 33
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    Western Blotting (WB), ELISA
    交叉反应
    人, 小鼠
    纯化方法
    Antigen affinity purification
    免疫原
    Synthetic peptide of Human GALC
    亚型
    IgG
    Top Product
    Discover our top product GALC Primary Antibody
  • 应用备注
    ELISA:1:1000-1:2000, WB:1:200-1:1000,
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C,-80 °C
    储存方法
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 抗原
    GALC (Galactosylceramidase (GALC))
    别名
    GALC (GALC 产品)
    别名
    2310068B06Rik antibody, A930008M05Rik antibody, AW212969 antibody, AW413532 antibody, Gacy antibody, twi antibody, twitcher antibody, galc antibody, galcl antibody, zgc:92561 antibody, si:ch211-199l3.4 antibody, GALCERase antibody, wu:fi04e07 antibody, zgc:56444 antibody, galactosylceramidase antibody, galactosylceramidase a antibody, Galactosylceramidase antibody, galactosylceramidase L homeolog antibody, galactosylceramidase b antibody, GALC antibody, Galc antibody, galca antibody, galc antibody, Caci_7107 antibody, Bacsa_1415 antibody, Spico_0384 antibody, LOC100304802 antibody, galc.L antibody, galcb antibody
    背景

    Background: This gene encodes a lysosomal protein which hydrolyzes the galactose ester bonds of galactosylceramide, galactosylsphingosine, lactosylceramide, and monogalactosyldiglyceride. Mutations in this gene have been associated with Krabbe disease, also known as globoid cell leukodystrophy. Alternate transcriptional splice variants, encoding different isoforms, have been characterized.

    Aliases: Gacy antibody, Galactocerebrosidase antibody, Galactocerebroside beta galactosidase antibody, Galactocerebroside beta-galactosidase antibody, Galactosylceramidase antibody, Galactosylceramide beta galactosidase antibody, Galactosylceramide beta-galactosidase antibody, galactosylceraminidase antibody, GALC antibody, GALC_HUMAN antibody, GALCERase antibody, Twitcher antibody

    UniProt
    P54803
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