GALC 抗体
Quick Overview for GALC 抗体 (ABIN7190741)
抗原
See all GALC 抗体适用
宿主
克隆类型
标记
应用范围
-
-
交叉反应
- 人, 小鼠
-
纯化方法
- Antigen affinity purification
-
免疫原
- Synthetic peptide of Human GALC
-
亚型
- IgG
-
-
-
-
应用备注
- ELISA:1:1000-1:2000, WB:1:200-1:1000,
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
缓冲液
- -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
-
储存液
- Sodium azide
-
注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
储存条件
- -20 °C,-80 °C
-
储存方法
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
-
-
- GALC (Galactosylceramidase (GALC))
-
别名
- GALC
-
背景
-
Background: This gene encodes a lysosomal protein which hydrolyzes the galactose ester bonds of galactosylceramide, galactosylsphingosine, lactosylceramide, and monogalactosyldiglyceride. Mutations in this gene have been associated with Krabbe disease, also known as globoid cell leukodystrophy. Alternate transcriptional splice variants, encoding different isoforms, have been characterized.
Aliases: Gacy antibody, Galactocerebrosidase antibody, Galactocerebroside beta galactosidase antibody, Galactocerebroside beta-galactosidase antibody, Galactosylceramidase antibody, Galactosylceramide beta galactosidase antibody, Galactosylceramide beta-galactosidase antibody, galactosylceraminidase antibody, GALC antibody, GALC_HUMAN antibody, GALCERase antibody, Twitcher antibody
-
UniProt
- P54803
抗原
-