ALDOA 抗体 (AA 2-364) (Biotin)
Quick Overview for ALDOA 抗体 (AA 2-364) (Biotin) (ABIN7153212)
抗原
See all ALDOA 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 2-364
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交叉反应
- 人
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纯化方法
- >95%, Protein G purified
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免疫原
- Recombinant Human Fructose-bisphosphate aldolase A protein (2-364AA)
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亚型
- IgG
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应用备注
- Optimal working dilution should be determined by the investigator.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
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Preservative: 0.03 % Proclin 300
Constituents: 50 % Glycerol, 0.01M PBS, PH 7.4 -
储存液
- ProClin
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注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C,-80 °C
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储存方法
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- ALDOA (Aldolase A, Fructose-Bisphosphate (ALDOA))
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别名
- ALDOA
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背景
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Background: Plays a key role in glycolysis and gluconeogenesis. In addition, may also function as scaffolding protein .Defects in ALDOA are the cause of glycogen storage disease type 12 (GSD12) [MIM:611881], also known as red cell aldolase deficiency. A metabolic disorder associated with increased hepatic glycogen and hemolytic anemia. It may lead to myopathy with exercise intolerance and rhabdomyolysis.Belongs to the class I fructose-bisphosphate aldolase family.
Aliases: ALDA antibody, Aldo1 antibody, ALDOA antibody, ALDOA_HUMAN antibody, Aldolase 1 antibody, Aldolase A antibody, Aldolase A fructose bisphosphatase antibody, Aldolase A fructose bisphosphate antibody, Aldolase, fructose-bisphosphate A antibody, Epididymis secretory sperm binding protein Li 87p antibody, FRUCTOALDOLASE A antibody, Fructose 1 6 bisphosphate triosephosphate lyase antibody, Fructose bisphosphate aldolase A antibody, Fructose bisphosphate aldolase antibody, FRUCTOSE-1,6-BISPHOSPHATE ALDOLASE A antibody, Fructose-bisphosphate aldolase A antibody, Fructose-bisphosphate aldolase A Muscle-type antibody, GSD12 antibody, HEL S 87p antibody, Lung cancer antigen NY LU 1 antibody, Lung cancer antigen NY-LU-1 antibody, MGC10942 antibody, MGC17716 antibody, MGC17767 antibody, Muscle type aldolase antibody, Muscle-type aldolase antibody, RNALDOG5 antibody
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UniProt
- P04075
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途径
- Ribonucleoside Biosynthetic Process
抗原
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