COX6B1 抗体 (AA 1-86)
Quick Overview for COX6B1 抗体 (AA 1-86) (ABIN7149179)
抗原
See all COX6B1 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 1-86
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交叉反应
- 人
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纯化方法
- >95%, Protein G purified
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免疫原
- Recombinant Human Cytochrome c oxidase subunit 6B1 protein (1-86AA)
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亚型
- IgG
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anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (AA 1-86) antibody
COX6B1 适用: 人 WB, IF 宿主: 小鼠 Polyclonal unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) antibodyCOX6B1 适用: 人, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (AA 1-86) antibodyCOX6B1 适用: 人 WB, ELISA, IHC (p) 宿主: 小鼠 Monoclonal 5D3 unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (AA 1-86) antibodyCOX6B1 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 2D3 unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (C-Term) antibodyCOX6B1 适用: 人 WB, IHC (p), IF, ICC 宿主: 兔 Polyclonal unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (AA 8-22), (N-Term) antibodyCOX6B1 适用: 人 WB, IF 宿主: 兔 Polyclonal RB48530 unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (AA 1-86) antibodyCOX6B1 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (AA 1-86) antibodyCOX6B1 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 5D3 unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) antibodyCOX6B1 适用: 人 WB, IHC 宿主: 兔 Monoclonal unconjugated
anti-Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1) (Internal Region) antibodyCOX6B1 适用: 人, 大鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
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应用备注
- Recommended dilution: IF:1:50-1:200,
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
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Preservative: 0.03 % Proclin 300
Constituents: 50 % Glycerol, 0.01M PBS, PH 7.4 -
储存液
- ProClin
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注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C,-80 °C
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储存方法
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))
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别名
- COX6B1
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背景
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Background: Defects in COX6B1 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110], also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.
Aliases: COX 6B antibody, COX VIb 1 antibody, COX VIb-1 antibody, COX6B antibody, COX6B1 antibody, COXG antibody, COXVIb1 antibody, CX6B1_HUMAN antibody, Cytochrome c oxidase subunit 6B1 antibody, Cytochrome c oxidase subunit VIb antibody, Cytochrome c oxidase subunit VIb isoform 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, Cytochrome c oxidase subunit Vib polypeptide 1 antibody
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UniProt
- P14854
抗原
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