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AGA 抗体

AGA 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7128282
发货至: 中国
  • 抗原 See all AGA 抗体
    AGA (Aspartylglucosaminidase (AGA))
    适用
    • 19
    • 11
    • 2
    • 2
    • 2
    • 2
    • 2
    • 2
    宿主
    • 19
    • 1
    克隆类型
    • 20
    多克隆
    标记
    • 9
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This AGA antibody is un-conjugated
    应用范围
    • 10
    • 6
    • 3
    • 2
    • 2
    • 1
    Western Blotting (WB), ELISA, Immunohistochemistry (IHC)
    交叉反应
    人, 小鼠, 大鼠
    纯化方法
    Antigen affinity purification
    免疫原
    Fusion protein of Human AGA
    亚型
    IgG
  • 应用备注
    ELISA:1:1000-1:2000, WB:1:200-1:1000, IHC:1:15-1:50,
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C,-80 °C
    储存方法
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 抗原
    AGA (Aspartylglucosaminidase (AGA))
    别名
    AGA (AGA 产品)
    别名
    AGU antibody, ASRG antibody, GA antibody, AW060726 antibody, aspartylglucosaminidase antibody, AGA antibody, Aga antibody
    背景

    Background: Aspartylglucosaminidase is involved in the catabolism of N-linked oligosaccharides of glycoproteins. It cleaves asparagine from N-acetylglucosamines as one of the final steps in the lysosomal breakdown of glycoproteins. The lysosomal storage disease aspartylglycosaminuria is caused by a deficiency in the AGA enzyme. Alternatively spliced transcript variants have been identified.

    Aliases: Aga antibody, AGU antibody, Aspartylglucosaminidase antibody, Aspartylglucosylamine deaspartylase antibody, Aspartylglycosaminuria antibody, ASPG_HUMAN antibody, ASRG antibody, GA antibody, Glycosylasparaginase antibody, Glycosylasparaginase beta chain antibody, N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase antibody, N4 (N acetyl beta glucosaminyl) L asparagine amidase antibody, N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase antibody

    UniProt
    P20933
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