AGA 抗体
Quick Overview for AGA 抗体 (ABIN7128282)
抗原
See all AGA 抗体适用
宿主
克隆类型
标记
应用范围
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    - 
                                            交叉反应
- 人, 小鼠, 大鼠
- 
                                            纯化方法
- Antigen affinity purification
- 
                                            免疫原
- Fusion protein of Human AGA
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                                            亚型
- IgG
 
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    - 
                                            应用备注
- ELISA:1:1000-1:2000, WB:1:200-1:1000, IHC:1:15-1:50,
- 
                                            限制
- 仅限研究用
 
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    - 
                                            状态
- Liquid
- 
                                            缓冲液
- -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
- 
                                            储存液
- Sodium azide
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                                            注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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                                            储存条件
- -20 °C,-80 °C
- 
                                            储存方法
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
 
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    - AGA (Aspartylglucosaminidase (AGA))
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                                            别名
- AGA
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                                            背景
- 
                        Background: Aspartylglucosaminidase is involved in the catabolism of N-linked oligosaccharides of glycoproteins. It cleaves asparagine from N-acetylglucosamines as one of the final steps in the lysosomal breakdown of glycoproteins. The lysosomal storage disease aspartylglycosaminuria is caused by a deficiency in the AGA enzyme. Alternatively spliced transcript variants have been identified. Aliases: Aga antibody, AGU antibody, Aspartylglucosaminidase antibody, Aspartylglucosylamine deaspartylase antibody, Aspartylglycosaminuria antibody, ASPG_HUMAN antibody, ASRG antibody, GA antibody, Glycosylasparaginase antibody, Glycosylasparaginase beta chain antibody, N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase antibody, N4 (N acetyl beta glucosaminyl) L asparagine amidase antibody, N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase antibody 
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                                            UniProt
- P20933
 抗原
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