SGSH 抗体
Quick Overview for SGSH 抗体 (ABIN7116690)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
-
-
原理
- SGSH antibody
-
纯化方法
- Immunogen affinity purified
-
纯度
- ≥95 % as determined by SDS-PAGE
-
免疫原
- N-sulfoglucosamine sulfohydrolase
-
亚型
- IgG
-
-
-
-
应用备注
- WB: 1:500 - 1:2000, IHC: 1:50 - 1:100
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
缓冲液
- PBS with 0.02 % sodium azide and 50 % glycerol pH 7.3,
-
储存液
- Sodium azide
-
注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
注意事项
- Avoid repeated freeze / thaw cycles.
-
储存条件
- -20 °C
-
储存方法
- -20°C for 12 months
-
有效期
- 12 months
-
-
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
-
别名
- SGSH
-
背景
-
Synonyms: N-sulphoglucosamine sulphohydrolase|Sulfoglucosamine sulfamidase|Sulphamidase|SGSH|HSS
Background: This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
-
分子量
- 57 kDa
-
基因ID
- 6448
-
UniProt
- P51688
-
途径
- Glycosaminoglycan Metabolic Process
抗原
-