PEX19 抗体
Quick Overview for PEX19 抗体 (ABIN7261435)
抗原
See all PEX19 抗体适用
宿主
克隆类型
标记
应用范围
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产品特性
- Polyclonal Antibody
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纯化方法
- Affinity purification
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免疫原
- Recombinant fusion protein of human PEX19 (NP_002848.1).
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亚型
- IgG
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anti-Peroxisomal Biogenesis Factor 19 (PEX19) antibody
PEX19 适用: 人 WB, IF, ICC, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Peroxisomal Biogenesis Factor 19 (PEX19) (AA 1-299) antibodyPEX19 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 2E4 unconjugated
anti-Peroxisomal Biogenesis Factor 19 (PEX19) (AA 1-299) antibodyPEX19 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Peroxisomal Biogenesis Factor 19 (PEX19) (AA 1-299) antibodyPEX19 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Peroxisomal Biogenesis Factor 19 (PEX19) (AA 1-299) antibodyPEX19 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Peroxisomal Biogenesis Factor 19 (PEX19) (C-Term) antibodyPEX19 适用: 人, 小鼠, 大鼠, 兔, 猴 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- IF 1:50-1:200
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 mg/mL
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缓冲液
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))
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别名
- PEX19
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背景
- This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants.
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基因ID
- 5824
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UniProt
- P40855
抗原
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