ETHE1 抗体
Quick Overview for ETHE1 抗体 (ABIN7255167)
抗原
See all ETHE1 抗体适用
宿主
克隆类型
标记
应用范围
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产品特性
- Polyclonal Antibody
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纯化方法
- Affinity purification
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免疫原
- Recombinant fusion protein of human ETHE1 (NP_055112.2).
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亚型
- IgG
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应用备注
- WB 1:200-1:1000 IHC 1:50-1:200 IF 1:50-1:200
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 mg/mL
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缓冲液
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))
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别名
- ETHE1
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背景
- This gene encodes a member of the metallo beta-lactamase family of iron-containing proteins involved in the mitochondrial sulfide oxidation pathway. The encoded protein catalyzes the oxidation of a persulfide substrate to sulfite. Certain mutations in this gene cause ethylmalonic encephalopathy, an infantile metabolic disorder affecting the brain, gastrointestinal tract and peripheral vessels. Alternative splicing results in multiple transcript variants encoding different isoforms.
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分子量
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Observed_MW: 28 kDa
Calculated_MW: 27 kDa
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基因ID
- 23474
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UniProt
- O95571
抗原
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