VMA21 抗体
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北京 101111
Quick Overview for VMA21 抗体 (ABIN7254226)
抗原
See all VMA21 抗体适用
宿主
克隆类型
标记
应用范围
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产品特性
- Polyclonal Antibody
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纯化方法
- Antigen affinity purification
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免疫原
- Synthetic peptide of human VMA21
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亚型
- IgG
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应用备注
- IHC 1:150-1:500, IF 1: 50-1:200, ELISA 1:5000-1:240000
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 2.6 mg/mL
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缓冲液
- PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- VMA21 (Vacuolar H+-ATPase Homolog (VMA21))
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别名
- VMA21
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背景
- This gene encodes a chaperone for assembly of lysosomal vacuolar ATPase. Required for the assembly of the V0 complex of the vacuolar ATPase (V-ATPase) in the endoplasmic reticulum. Associates with the V0 complex of the vacuolar ATPase (V-ATPase). MEAX is a childhood-onset disease characterized by progressive vacuolation and atrophy of skeletal muscle. It is inherited in recessive fashion, affecting boys and sparing carrier females. Onset is in childhood, and patients exhibit weakness of the proximal muscles of the lower extremities, progressing slowly to involve other skeletal muscle groups over time.
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UniProt
- Q3ZAQ7
抗原
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