BCKDHA 抗体
Quick Overview for BCKDHA 抗体 (ABIN6572016)
抗原
See all BCKDHA 抗体适用
宿主
克隆类型
标记
应用范围
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纯化方法
- Affinity purification
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免疫原
- Recombinant protein of human BCKDHA
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亚型
- IgG
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anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) (AA 268-407) antibody
BCKDHA 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) (AA 347-445) antibodyBCKDHA 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) (AA 362-390), (C-Term) antibodyBCKDHA 适用: 人 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB20924 unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) (AA 1-445) antibodyBCKDHA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) (AA 71-120) antibodyBCKDHA 适用: 人, 小鼠, 大鼠, 豚鼠, 兔, Cow, 马, 绵羊, 猴, Pig, 非洲爪蟾 WB 宿主: 兔 Polyclonal unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) (N-Term) antibodyBCKDHA 适用: 人, 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- WB 1:500 - 1:2000
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限制
- 仅限研究用
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浓度
- 1 mg/mL
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缓冲液
- Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- BCKDHA (Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))
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别名
- BCKDHA
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背景
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Synonyms: Branched chain alpha keto acid dehydrogenase E1 component alpha polypeptide, FLJ45695, OVD1A,2 oxoisovalerate dehydrogenase (lipoamide),2 oxoisovalerate dehydrogenase subunit alpha, mitochondrial ,2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial,BCKDE1A,BCKDH E1 alpha,BCKDH E1-alpha,BCKDHA,Branched chain alpha keto acid dehydrogenase E1 component alpha chain,Branched chain keto acid dehydrogenase E1 alpha polypeptide,Branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease),Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain,MSU,MSUD1,ODBA
Background: The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.
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分子量
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Observed_MW: 50kDa
Calculated_MW: 50kDa
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基因ID
- 593
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UniProt
- P12694
抗原
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