Frataxin 抗体
Quick Overview for Frataxin 抗体 (ABIN6568875)
抗原
See all Frataxin (FXN) 抗体适用
宿主
克隆类型
标记
应用范围
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纯化方法
- Affinity purification
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免疫原
- Recombinant protein of human FXN
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亚型
- IgG
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应用备注
- WB 1:500 - 1:2000 IHC 1:50 - 1:200 IF 1:50 - 1:200
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限制
- 仅限研究用
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浓度
- 1 mg/mL
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缓冲液
- Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- Frataxin (FXN)
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别名
- FXN
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背景
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Synonyms: CyaY,d-FXN,FA,FARR,Frataxin mature form,Frataxin(81-210),FRDA,FRDA,Friedreich ataxia protein,Fxn,i-FXN,m56-FXN,m78-FXN,m81-FXN,MGC57199,X25
Background: This nuclear gene encodes a mitochondrial protein which belongs to the FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA from 8-33 repeats to >90 repeats results in Friedreich ataxia. Alternative splicing results in multiple transcript variants.
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分子量
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Observed_MW: 14kDa
Calculated_MW: 19kDa/21kDa/23kDa
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基因ID
- 2395
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UniProt
- Q16595
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途径
- Transition Metal Ion Homeostasis, Regulation of Cell Size
抗原
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