FAH 抗体
Quick Overview for FAH 抗体 (ABIN6568002)
抗原
See all FAH 抗体适用
宿主
克隆类型
标记
应用范围
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纯化方法
- Affinity purification
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免疫原
- Recombinant fusion protein of human FAH (NP_000128.1).
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亚型
- IgG
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应用备注
- WB 1:500-1:2000 IHC 1:50-1:200
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 mg/mL
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缓冲液
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- FAH (Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH))
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别名
- FAH
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背景
- This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT).
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分子量
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Observed_MW: 40kDa
Calculated_MW: 38kDa/46kDa
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基因ID
- 2184
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UniProt
- P16930
抗原
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