SGSH 抗体 (C-Term)
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Quick Overview for SGSH 抗体 (C-Term) (ABIN653531)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
克隆位点
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抗原表位
- AA 420-449, C-Term
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纯化方法
- This antibody is purified through a protein A column, followed by peptide affinity purification.
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免疫原
- This SGSH antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 420-449 amino acids from the C-terminal region of human SGSH.
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亚型
- Ig Fraction
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应用备注
- WB: 1:4000
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- 4 °C,-20 °C
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储存方法
- Maintain refrigerated at 2-8 °C for up to 6 months. For long term storage store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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有效期
- 6 months
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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别名
- SGSH
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背景
- SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
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分子量
- 56695
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基因ID
- 6448
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NCBI登录号
- NP_000190
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UniProt
- P51688
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途径
- Glycosaminoglycan Metabolic Process
抗原
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