GCDH 抗体 (AA 149-438)
Quick Overview for GCDH 抗体 (AA 149-438) (ABIN6141009)
抗原
See all GCDH 抗体适用
宿主
克隆类型
标记
应用范围
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    - 
                                            抗原表位
- AA 149-438
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                                            序列
- MHPIYAYGSE EQRQKYLPQL AKGELLGCFG LTEPNSGSDP SSMETRAHYN SSNKSYTLNG TKTWITNSPM ADLFVVWARC EDGCIRGFLL EKGMRGLSAP RIQGKFSLRA SATGMIIMDG VEVPEENVLP GASSLGGPFG CLNNARYGIA WGVLGASEFC LHTARQYALD RMQFGVPLAR NQLIQKKLAD MLTEITLGLH ACLQLGRLKD QDKAAPEMVS LLKRNNCGKA LDIARQARDM LGGNGISDEY HVIRHAMNLE AVNTYEGTHD IHALILGRAI TGIQAFTASK
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                                            交叉反应
- 人, 小鼠, 大鼠
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                                            产品特性
- Polyclonal Antibodies
- 
                                            纯化方法
- Affinity purification
- 
                                            免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 149-438 of human GCDH (NP_000150.1).
- 
                                            亚型
- IgG
 
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    - 
                                            应用备注
- WB,1:200 - 1:2000
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                                            说明
- 
                        HIGH QUALITY 
- 
                                            限制
- 仅限研究用
 
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- 
    - 
                                            状态
- Liquid
- 
                                            缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
- 
                                            储存液
- Sodium azide
- 
                                            注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 
                                            储存条件
- -20 °C
- 
                                            储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
 
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    - GCDH (Glutaryl-CoA Dehydrogenase (GCDH))
- 
                                            别名
- GCDH
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                                            背景
- The protein encoded by this gene belongs to the acyl-CoA dehydrogenase family. It catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and CO(2) in the degradative pathway of L-lysine, L-hydroxylysine, and L-tryptophan metabolism. It uses electron transfer flavoprotein as its electron acceptor. The enzyme exists in the mitochondrial matrix as a homotetramer of 45-kD subunits. Mutations in this gene result in the metabolic disorder glutaric aciduria type 1, which is also known as glutaric acidemia type I. Alternative splicing of this gene results in multiple transcript variants. A related pseudogene has been identified on chromosome 12.,GCDH,ACAD5,GCD,Cancer,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,GCDH
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                                            分子量
- 47 kDa/48 kDa
- 
                                            基因ID
- 2639
- 
                                            UniProt
- Q92947
 抗原
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