FKRP 抗体 (AA 30-220)
Quick Overview for FKRP 抗体 (AA 30-220) (ABIN6140666)
抗原
See all FKRP 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 30-220
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序列
- QPRNSRARGP RRASAAGPRV TVLVREFEAF DNAVPELVDS FLQQDPAQPV VVAADTLPYP PLALPRIPNV RLALLQPALD RPAAASRPET YVATEFVALV PDGARAEAPG LLERMVEALR AGSARLVAAP VATANPARCL ALNVSLREWT ARYGAAPAAP RCDALDGDAV VLLRARDLFN LSAPLARPVG T
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交叉反应
- 人, 小鼠, 大鼠
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产品特性
- Polyclonal Antibodies
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纯化方法
- Affinity purification
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免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 30-220 of human FKRP (NP_077277.1).
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亚型
- IgG
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应用备注
- WB,1:1000 - 1:3000,IHC,1:50 - 1:200
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说明
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HIGH QUALITY
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- FKRP (Fukutin Related Protein (FKRP))
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别名
- FKRP
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背景
- This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined.,FKRP,LGMD2I,MDC1C,MDDGA5,MDDGB5,MDDGC5,Signal Transduction,FKRP
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分子量
- 54 kDa
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基因ID
- 79147
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UniProt
- Q9H9S5
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途径
- Regulation of Carbohydrate Metabolic Process
抗原
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