CLCN1 抗体 (AA 779-988)
Quick Overview for CLCN1 抗体 (AA 779-988) (ABIN6138661)
抗原
See all CLCN1 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 779-988
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序列
- ARPTKKKTTQ DSTDLVDNMS PEEIEAWEQE QLSQPVCFDS CCIDQSPFQL VEQTTLHKTH TLFSLLGLHL AYVTSMGKLR GVLALEELQK AIEGHTKSGV QLRPPLASFR NTTSTRKSTG APPSSAENWN LPEDRPGATG TGDVIAASPE TPVPSPSPEP PLSLAPGKVE GELEELELVE SPGLEEELAD ILQGPSLRST DEEDEDELIL
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交叉反应
- 人, 小鼠, 大鼠
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产品特性
- Polyclonal Antibodies
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纯化方法
- Affinity purification
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免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 779-988 of human CLCN1 (NP_000074.2).
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亚型
- IgG
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应用备注
- WB,1:500 - 1:2000,IHC,1:50 - 1:200
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说明
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HIGH QUALITY
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- CLCN1 (Chloride Channel 1, Skeletal Muscle (CLCN1))
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别名
- CLCN1
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背景
- The CLCN family of voltage-dependent chloride channel genes comprises nine members (CLCN1-7, Ka and Kb) which demonstrate quite diverse functional characteristics while sharing significant sequence homology. The protein encoded by this gene regulates the electric excitability of the skeletal muscle membrane. Mutations in this gene cause two forms of inherited human muscle disorders: recessive generalized myotonia congenita (Becker) and dominant myotonia (Thomsen). Alternative splicing results in multiple transcript variants.,CLCN1,CLC1,Signal Transduction,Endocrine & Metabolism,Neuroscience,CLCN1
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分子量
- 108 kDa
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基因ID
- 1180
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UniProt
- P35523
抗原
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