Hexosaminidase A 抗体 (AA 89-529)
Quick Overview for Hexosaminidase A 抗体 (AA 89-529) (ABIN5775909)
抗原
See all Hexosaminidase A (HEXA) 抗体适用
宿主
克隆类型
标记
应用范围
克隆位点
-
-
抗原表位
- AA 89-529
-
免疫原
- Recombinant human HEXA (89-529aa) purified from E. coli
-
亚型
- IgG2a lambda
-
-
anti-Hexosaminidase A (HEXA) (AA 318-529) antibody
HEXA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Hexosaminidase A (HEXA) (Internal Region) antibodyHEXA 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Hexosaminidase A (HEXA) (AA 1-529) antibodyHEXA 适用: 人 WB, ELISA, IF 宿主: 小鼠 Monoclonal 3D1 unconjugated
anti-Hexosaminidase A (HEXA) antibodyHEXA 适用: 人 WB, ELISA, FACS 宿主: 小鼠 Monoclonal 3F10 unconjugated
anti-Hexosaminidase A (HEXA) (AA 142-170), (N-Term) antibodyHEXA 适用: 人, 小鼠 WB, FACS, IHC (p) 宿主: 兔 Polyclonal RB20977 unconjugated
anti-Hexosaminidase A (HEXA) (AA 1-529) antibodyHEXA 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 3D1 unconjugated
anti-Hexosaminidase A (HEXA) antibodyHEXA 适用: 人, 小鼠, 大鼠 WB, ELISA, FACS 宿主: 小鼠 Monoclonal unconjugated
anti-Hexosaminidase A (HEXA) (AA 319-528) antibodyHEXA 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Hexosaminidase A (HEXA) (AA 89-529) antibodyHEXA 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Hexosaminidase A (HEXA) antibodyHEXA 适用: 人 WB, FACS, EIA 宿主: 小鼠 Monoclonal 3F10 unconjugated
-
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
浓度
- 1 mg/mL
-
储存条件
- 4 °C,-20 °C,-80 °C
-
储存方法
- Can be stored at +2°C to +8°C for 1 week. For long term storage, aliquot and store at -20°C to -80°C. Avoid repeated freezing and thawing cycles.
-
-
- Hexosaminidase A (HEXA)
-
别名
- Hexosaminidase A/HEXA
-
背景
- HEXA (Hexosaminidase A), also designated beta-Hexosaminidase A, is responsible for the degradation of GM2 gangliosides, and a variety of other molecules containing terminal N-acetyl hexosamines, in the brain and other tissues. A mutation in the a subunit of hexosaminidase is the cause of Tay-Sachs disease (TSD), also known as GM2-gangliosidosis type I. TSD is a fatal autosomal recessive lysosomal storage disease of the central nervous system (CNS) caused by insufficient activity of the HEXA enzyme that results in a failure to process GM2 gangliosides. The accumulation of GM2 ganglioside in the absence of HEXA activity causes progressive destruction of the CNS.
-
NCBI登录号
- NP_000511
-
途径
- Sensory Perception of Sound, Glycosaminoglycan Metabolic Process
抗原
-
