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Aminoacylase 1 抗体 (AA 1-408)

This anti-Aminoacylase 1 antibody is a 小鼠 单克隆 antibody detecting Aminoacylase 1 in WB, ELISA, FACS, IF 和 ICC. Suitable for 人.
产品编号 ABIN5775904
发货至: 中国

Quick Overview for Aminoacylase 1 抗体 (AA 1-408) (ABIN5775904)

抗原

See all Aminoacylase 1 (ACY1) 抗体
Aminoacylase 1 (ACY1)

适用

  • 34
  • 14
  • 4
  • 2
  • 1
  • 1

宿主

  • 22
  • 13
  • 2
小鼠

克隆类型

  • 24
  • 13
单克隆

标记

  • 30
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
This Aminoacylase 1 antibody is un-conjugated

应用范围

  • 28
  • 15
  • 13
  • 7
  • 7
  • 6
  • 5
  • 3
  • 2
  • 1
  • 1
  • 1
  • 1
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  • 1
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Western Blotting (WB), ELISA, Flow Cytometry (FACS), Immunofluorescence (IF), Immunocytochemistry (ICC)

克隆位点

AT1E2
  • 抗原表位

    • 10
    • 3
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 1-408

    免疫原

    Recombinant human ACY1 (1-408aa) purified from E. coli

    亚型

    IgG2b kappa
  • 限制

    仅限研究用
  • 状态

    Liquid

    浓度

    1 mg/mL

    储存条件

    4 °C,-20 °C,-80 °C

    储存方法

    Can be stored at +2°C to +8°C for 1 week. For long term storage, aliquot and store at -20°C to -80°C. Avoid repeated freezing and thawing cycles.
  • 抗原

    Aminoacylase 1 (ACY1)

    别名

    Aminoacylase/ACY1

    背景

    Aminoacylase-1, also designated N-acyl-L-amino-acid amidohydrolase or ACY1, is a member of the largest metallopeptidase family called M20A. Aminoacylase-1 is a zinc-binding homodimeric enzyme expressed in kidney, brain, placenta and spleen. It is the most abundant of the aminoacylases. Defects in ACY1 are the cause of aminoacylase-1 deficiency (ACY1D). ACY1D results in a metabolic disorder manifesting with encephalopathy, unspecific psychomotor delay, psychomotor delay with atrophy of the vermis and syringomyelia, marked muscular hypotonia or normal clinical features. All affected individuals exhibit markedly increased urinary excretion of several N-acetylated amino acids.

    NCBI登录号

    NP_000657
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