PEX19 抗体
Quick Overview for PEX19 抗体 (ABIN5704133)
抗原
See all PEX19 抗体适用
宿主
克隆类型
标记
应用范围
-
-
免疫原
- peroxisomal biogenesis factor 19
-
亚型
- IgG
-
-
-
-
应用备注
- WB : 1:200-1:2000 IP : 1:200-1:1000 IHC : 1:20-1:200
-
说明
-
human heart tissue were subjected to SDS PAGE followed by western blot with FNab06329(PEX19 antibody) at dilution of 1:300
-
限制
- 仅限研究用
-
-
-
缓冲液
- PBS with 0.02 % sodium azide and 50 % glycerol pH 7.3
-
储存液
- Sodium azide
-
注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
注意事项
- Avoid repeated freeze / thaw cycles.
-
储存条件
- -20 °C
-
有效期
- 12 months
-
-
- PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))
-
别名
- PEX19
-
背景
- Synonyms:33 kDa housekeeping protein, D1S2223E, HK33, Peroxin 19, PEX19, PMP1, PMPI, PXF, PXMP1 Background:This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants.
-
分子量
- 35-40 kDa
-
基因ID
- 5824
-
UniProt
- P40855
抗原
-