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CHRND 抗体 (AA 22-245)

CHRND 适用: 人 WB, ELISA, FACS, IHC, ICC, Neut 宿主: 小鼠 Monoclonal 1H1F9 unconjugated
产品编号 ABIN5611361
发货至: 中国
  • 抗原 See all CHRND 抗体
    CHRND (Cholinergic Receptor, Nicotinic, delta (Muscle) (CHRND))
    抗原表位
    • 7
    • 7
    • 6
    • 6
    • 4
    • 4
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 22-245
    适用
    • 33
    • 6
    • 5
    • 5
    • 4
    • 3
    • 3
    • 3
    • 3
    • 2
    • 1
    • 1
    宿主
    • 32
    • 1
    小鼠
    克隆类型
    • 32
    • 1
    单克隆
    标记
    • 20
    • 3
    • 3
    • 3
    • 2
    • 2
    This CHRND antibody is un-conjugated
    应用范围
    • 27
    • 20
    • 13
    • 3
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    Western Blotting (WB), ELISA, Flow Cytometry (FACS), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Neutralization (Neut)
    纯化方法
    purified
    免疫原
    Purified recombinant fragment of human CHRND (AA: extra 22-245) expressed in E. coli.
    克隆位点
    1H1F9
    亚型
    IgG1
  • 应用备注
    ELISA: 1:10000, WB: 1:500 - 1:2000, ICC: N/A, FCM: 1:200 - 1:400, IHC: N/A
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    Purified antibody in PBS with 0.05 % sodium azide
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    4 °C/-20 °C
    储存方法
    4°C, -20°C for long term storage
  • 抗原
    CHRND (Cholinergic Receptor, Nicotinic, delta (Muscle) (CHRND))
    别名
    CHRND (CHRND 产品)
    别名
    ACHRD antibody, CMS2A antibody, FCCMS antibody, SCCMS antibody, wu:fa01e01 antibody, zgc:110469 antibody, CHNRD antibody, MGC97613 antibody, Achr-4 antibody, Acrd antibody, L10076 antibody, chnrd antibody, chrng antibody, cholinergic receptor nicotinic delta subunit antibody, cholinergic receptor, nicotinic, delta (muscle) antibody, cholinergic receptor, nicotinic, delta antibody, cholinergic receptor nicotinic gamma subunit antibody, cholinergic receptor, nicotinic delta antibody, cholinergic receptor, nicotinic, delta polypeptide antibody, cholinergic receptor, nicotinic delta L homeolog antibody, CHRND antibody, chrnd antibody, CHRNG antibody, Chrnd antibody, chrnd.L antibody
    背景

    Description: The acetylcholine receptor of muscle has 5 subunits of 4 different types: 2 alpha and 1 each of beta, gamma and delta subunits. After acetylcholine binding, the receptor undergoes an extensive conformation change that affects all subunits and leads to opening of an ion-conducting channel across the plasma membrane. Defects in this gene are a cause of multiple pterygium syndrome lethal type (MUPSL), congenital myasthenic syndrome slow-channel type (SCCMS), and congenital myasthenic syndrome fast-channel type (FCCMS). Several transcript variants encoding different isoforms have been found for this gene.

    Aliases: ACHRD, CMS2A, CMS3A, CMS3B, CMS3C, FCCMS, SCCMS

    分子量
    58.8 kDa
    基因ID
    1144
    HGNC
    1144
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