NAGLU 抗体 (C-Term)
Our Local Distributor
北京 101111
Quick Overview for NAGLU 抗体 (C-Term) (ABIN5517086)
抗原
See all NAGLU 抗体适用
宿主
克隆类型
标记
应用范围
-
-
抗原表位
- C-Term
-
序列
- LEALVDSVAQ GIPFQQHQFD KNVFQLEQAF VLSKQRYPSQ PRGDTVDLAK
-
纯化方法
- Affinity purified
-
免疫原
- The immunogen is a synthetic peptide directed towards the C terminal region of human NAGLU
-
-
-
-
应用备注
- Optimal working dilution should be determined by the investigator.
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
-
储存液
- Sodium azide
-
注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
储存条件
- -20 °C
-
储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
-
-
- NAGLU (N-Acetylglucosaminidase, alpha (NAGLU))
-
别名
- NAGLU
-
背景
-
This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate.
Alias Symbols: NAG, MPS3B, UFHSD, MPS-IIIB
Protein Size: 639 -
基因ID
- 4669
-
NCBI登录号
- NM_000263, NP_000254
-
UniProt
- P54802
-
途径
- Glycosaminoglycan Metabolic Process
抗原
-