IDUA 抗体 (N-Term)
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Quick Overview for IDUA 抗体 (N-Term) (ABIN5514526)
抗原
See all IDUA 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- N-Term
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序列
- LAHVSKWNFE TWNEPDHHDF DNVSMTMQGF LNYYDACSEG LRAASPALRL
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产品特性
- This is a rabbit polyclonal antibody against IDUA. It was validated on Western Blot.
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纯化方法
- Affinity purified
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免疫原
- The immunogen is a synthetic peptide directed towards the N-terminal region of Human IDUA
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应用备注
- Optimal working dilution should be determined by the investigator.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- IDUA (Iduronidase, alpha-L- (IDUA))
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别名
- IDUA
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背景
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This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
Alias Symbols: IDUA,
Protein Interaction Partner: MPP3,
Protein Size: 653 -
基因ID
- 3425
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NCBI登录号
- NP_000194
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UniProt
- P35475
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途径
- Glycosaminoglycan Metabolic Process
抗原
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