Peroxisomal Bifunctional Enzyme 抗体 (Middle Region)
Quick Overview for Peroxisomal Bifunctional Enzyme 抗体 (Middle Region) (ABIN5514454)
抗原
适用
宿主
克隆类型
应用范围
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抗原表位
- Middle Region
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序列
- VIAVDSDKNQ LATANKMITS VLEKEASKMQ QSGHPWSGPK PRLTSSVKEL
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产品特性
- This is a rabbit polyclonal antibody against ECHP. It was validated on Western Blot.
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纯化方法
- Affinity purified
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免疫原
- The immunogen is a synthetic peptide directed towards the middle region of Human ECHP
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应用备注
- Optimal working dilution should be determined by the investigator.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Peroxisomal Bifunctional Enzyme (ECHP)
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别名
- ECHP
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背景
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The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: EHHADH, ECHD,
Protein Size: 723 -
基因ID
- 1962
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NCBI登录号
- NP_001957
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UniProt
- Q08426
抗原
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