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LEPRE1 抗体 (AA 1-390)

Name: LEPRE1 抗体 (AA 1-390)
SKU: ABIN528557
Availability: OutOfStock

This anti-LEPRE1 antibody is a 小鼠多克隆 antibody detecting LEPRE1 in WB. Suitable for 人. This Primary Antibody has been cited in 9+ publications.

LEPRE1 MaxPab polyclonal antibody. (LEPRE1 抗体 (AA 1-390))

Western Blot analysis of LEPRE1 expression in transfected 293T cell line by LEPRE1 MaxPab polyclonal antibody. (LEPRE1 抗体 (AA 1-390))

2 images

(9 references)

产品编号 ABIN528557

发货至: 中国

Datasheet as PDF

Quick Overview for LEPRE1 抗体 (AA 1-390) (ABIN528557)

抗原

See all LEPRE1 抗体

LEPRE1 (Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1))

适用

人

宿主

小鼠

克隆类型

多克隆

标记

This LEPRE1 antibody is un-conjugated

应用范围

Western Blotting (WB)

Discover our top product LEPRE1 Primary Antibody

抗原表位
6

3

1

1

1
AA 1-390

原理

Mouse polyclonal antibody raised against a full-length human LEPRE1 protein.

序列

MLGEEHTRSI GPRESAKEYR QRSLLEKELL FFAYDVFGIP FVDPDSWTPE EVIPKRLQEK QKSERETAVR ISQEIGNLMK EIETLVEEKT KESLDVSRLT REGGPLLYEG ISLTMNSKLL NGSQRVVMDG VISDHECQEL QRLTNVAATS GDGYRGQTSP HTPNEKFYGV TVFKALKLGQ EGKVPLQSAH LYYNVTEKVR RIMESYFRLD TPLYFSYSHL VCRTAIEEVQ AERKDDSHPV HVDNCILNAE TLVCVKEPPA YTFRDYSAIL YLNGDFDGGN FYFTELDAKT VTAEVQPQCG RAVGFSSGTE NPHGVKAVTR GQRCAIALWF TLDPRHSERD RVQADDLVKM LFSPEEMDLS QEQPLDAQQG PPEPAQESLS GSESKPKDEL

交叉反应

人

产品特性

Antibody reactive against mammalian transfected lysate.

免疫原

LEPRE1 (AAH15309, 1 a.a. ~ 390 a.a) full-length human protein.
anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) (AA 1-100) antibody
LEPRE1 适用: 人 WB, ELISA, IF, IHC (p) 宿主: 小鼠 Monoclonal 3C7 unconjugated

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) antibody
LEPRE1 适用: 人 WB, FACS, IHC, IHC (p) 宿主: 小鼠 Monoclonal 1A1 unconjugated

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) antibody
LEPRE1 适用: 人 WB, FACS, IF 宿主: 小鼠 Monoclonal 1B4 unconjugated

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) (AA 499-533) antibody
LEPRE1 适用: 人 WB 宿主: 兔 Polyclonal RB49867 unconjugated

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) (AA 1-390) antibody
LEPRE1 适用: 人 WB 宿主: 兔 Polyclonal unconjugated

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) (AA 497-736) antibody
LEPRE1 适用: 人 WB 宿主: 兔 Polyclonal unconjugated

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) antibody
LEPRE1 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal unconjugated

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) (C-Term) antibody (HRP)
LEPRE1 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal HRP

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) (C-Term) antibody (PE)
LEPRE1 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal PE

anti-Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1) (C-Term) antibody (FITC)
LEPRE1 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal FITC

应用备注

Optimal working dilution should be determined by the investigator.

限制

仅限研究用
缓冲液

In 1x PBS, pH 7.4

注意事项

Aliquot to avoid repeated freezing and thawing.

储存条件

-20 °C

储存方法

Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
Huang, Mei, Lv, Li, Zhang, Pan, Tan, Guo, Luo, Chen, Liang, Wu: "Targeted exome sequencing identifies novel compound heterozygous mutations in P3H1 in a fetus with osteogenesis imperfecta type VIII." in: Clinica chimica acta; international journal of clinical chemistry, Vol. 464, pp. 170-175, (2016) (PubMed).

Cabral, Perdivara, Weis, Terajima, Blissett, Chang, Perosky, Makareeva, Mertz, Leikin, Tomer, Kozloff, Eyre, Yamauchi, Marini: "Abnormal type I collagen post-translational modification and crosslinking in a cyclophilin B KO mouse model of recessive osteogenesis imperfecta." in: PLoS genetics, Vol. 10, Issue 6, pp. e1004465, (2014) (PubMed).

Takagi, Ishii, Barnes, Weis, Amano, Tanaka, Fukuzawa, Nishimura, Eyre, Marini, Hasegawa: "A novel mutation in LEPRE1 that eliminates only the KDEL ER- retrieval sequence causes non-lethal osteogenesis imperfecta." in: PLoS ONE, Vol. 7, Issue 5, pp. e36809, (2012) (PubMed).

Pyott, Schwarze, Christiansen, Pepin, Leistritz, Dineen, Harris, Burton, Angle, Kim, Sussman, Weis, Eyre, Russell, McCarthy, Steiner, Byers: "Mutations in PPIB (cyclophilin B) delay type I procollagen chain association and result in perinatal lethal to moderate osteogenesis imperfecta phenotypes." in: Human molecular genetics, Vol. 20, Issue 8, pp. 1595-609, (2011) (PubMed).

Amor, Rauch, Gruenwald, Weis, Eyre, Roughley, Glorieux, Morello: "Severe osteogenesis imperfecta caused by a small in-frame deletion in CRTAP." in: American journal of medical genetics. Part A, Vol. 155A, Issue 11, pp. 2865-70, (2011) (PubMed).

Baldridge, Lennington, Weis, Homan, Jiang, Munivez, Keene, Hogue, Pyott, Byers, Krakow, Cohn, Eyre, Lee, Morello: "Generalized connective tissue disease in Crtap-/- mouse." in: PLoS ONE, Vol. 5, Issue 5, pp. e10560, (2010) (PubMed).

Willaert, Malfait, Symoens, Gevaert, Kayserili, Megarbane, Mortier, Leroy, Coucke, De Paepe: "Recessive osteogenesis imperfecta caused by LEPRE1 mutations: clinical documentation and identification of the splice form responsible for prolyl 3-hydroxylation." in: Journal of medical genetics, Vol. 46, Issue 4, pp. 233-41, (2009) (PubMed).

van Dijk, Nesbitt, Zwikstra, Nikkels, Piersma, Fratantoni, Jimenez, Huizer, Morsman, Cobben, van Roij, Elting, Verbeke, Wijnaendts, Shaw, Högler, McKeown, Sistermans, Dalton, Meijers-Heijboer, Pals: "PPIB mutations cause severe osteogenesis imperfecta." in: American journal of human genetics, Vol. 85, Issue 4, pp. 521-7, (2009) (PubMed).

Chang, Barnes, Cabral, Bodurtha, Marini: "Prolyl 3-hydroxylase 1 and CRTAP are mutually stabilizing in the endoplasmic reticulum collagen prolyl 3-hydroxylation complex." in: Human molecular genetics, Vol. 19, Issue 2, pp. 223-34, (2009) (PubMed).
抗原

LEPRE1 (Leucine Proline-Enriched Proteoglycan (Leprecan) 1 (LEPRE1))

别名

LEPRE1

背景

Full Gene Name: leucine proline-enriched proteoglycan (leprecan) 1
Synonyms: GROS1,MGC117314,P3H1

基因ID

64175