SGSH 抗体 (AA 301-388) (AbBy Fluor® 750)
Quick Overview for SGSH 抗体 (AA 301-388) (AbBy Fluor® 750) (ABIN5010457)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 301-388
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交叉反应
- 大鼠
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预测反应
- Human,Mouse,Dog
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纯化方法
- Purified by Protein A.
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免疫原
- KLH conjugated synthetic peptide derived from human Sulphamidase
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亚型
- IgG
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anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 21-389) antibody
SGSH 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibodySGSH 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibodySGSH 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (C-Term) antibodySGSH 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 301-388) antibodySGSH 适用: 大鼠 WB, ELISA, ICC, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibodySGSH 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 44-200) antibodySGSH 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibodySGSH 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (N-Term) antibodySGSH 适用: 人, 大鼠, 小鼠, Cow, 马, 犬, Pig, 豚鼠 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
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IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 -
限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 μg/μL
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缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
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储存液
- ProClin
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注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
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有效期
- 12 months
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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别名
- SGSH/Sulphamidase
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背景
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Synonyms: HSS, SFMD, MPS3A, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase, Sulphamidase, SGSH
Background: Sulfatases are enzymes that hydrolyse a diverse range of sulfate esters. Deficiency of lysosomal sulfatases leads to human diseases characterized by the accumulation of either GAGs (glycosaminoglycans) or sulfolipids. Sulfamidase, also known as HSS, SFMD, MPS3A or SGSH, is a 502 amino acid lysosome that belongs to the sulfatase family. It has been suggested that sulfamidase may be involved in the lysosomal degradation of heparan sulfate. Defects in the gene encoding sulfamidase are the cause of Sanfilippo syndrome A, an autosomal recessive lysosomal storage disease caused by impaired degradation of heparan sulfate. Sanfilippo syndrome A is characterized by severe central nervous system degeneration but relatively mild somatic manifestations.
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基因ID
- 6448
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UniProt
- P51688
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途径
- Glycosaminoglycan Metabolic Process
抗原
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