HPS3 抗体 (C-Term)
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Quick Overview for HPS3 抗体 (C-Term) (ABIN374450)
抗原
See all HPS3 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- C-Term
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序列
- PYLLYCSRKK PLT
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特异性
- This antibody recognizes HPS3/Cocoa
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交叉反应 （详细）
- Species reactivity (tested):Human.
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纯化方法
- Ammonium Sulphate Precipitation followed by antigen Affinity Chromatography using the immunizing peptide.
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免疫原
- Peptide from the C Terminus of the protein sequence according to NP_115759
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anti-Hermansky-Pudlak Syndrome 3 (HPS3) (C-Term) antibody
HPS3 适用: 人 WB, IHC (p), IF, ICC 宿主: 兔 Polyclonal unconjugated
anti-Hermansky-Pudlak Syndrome 3 (HPS3) (C-Term) antibodyVerified HPS3 适用: 人 WB, ELISA 宿主: 山羊 Polyclonal unconjugated
anti-Hermansky-Pudlak Syndrome 3 (HPS3) (AA 1-372) antibodyHPS3 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Hermansky-Pudlak Syndrome 3 (HPS3) (AA 51-100) antibodyHPS3 适用: 人, 大鼠, 小鼠, Cow, 豚鼠, 马, 兔, 斑马鱼, 猴, Pig WB 宿主: 兔 Polyclonal unconjugated
anti-Hermansky-Pudlak Syndrome 3 (HPS3) (N-Term) antibodyHPS3 适用: 人, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
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Peptide ELISA: > 1/32,000. Western Blot: 1-3 μg/mL. Detects a band of Approx 110 kDa in A431 cell lysate(Predicted Molecular Weight: 114 kDa).
Other applications not tested.
Optimal dilutions are dependent on conditions and should be determined by the user. -
限制
- 仅限研究用
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浓度
- 0.5 mg/mL
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缓冲液
- Tris saline, pH 7.3 containing 0.02 % Sodium Azide as preservative and 0.5 % BSA as stabilizer.
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储存液
- Sodium azide
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注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- Avoid repeated freezing and thawing.
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储存条件
- -20 °C
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储存方法
- Store the antibody (in aliquots) at -20 °C.
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- HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
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别名
- HPS3
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背景
- HPS3 is involved in early stages of melanosome biogenesis and maturation. Defects in HPS3 are the cause of the cocoa (coa) mutant, and of Hermansky-Pudlak syndrome type 3 (HPS3). HPS3 is an autosomal recessive disorder, characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.Synonyms: Hermansky-Pudlak syndrome 3
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基因ID
- 84343
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NCBI登录号
- NP_115759
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UniProt
- Q969F9
抗原
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