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GCS1 抗体 (C-Term)

MOGS 适用: 人, 小鼠 WB, EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN357670
发货至: 中国
  • 抗原 See all GCS1 (MOGS) 抗体
    GCS1 (MOGS) (Mannosyl-Oligosaccharide Glucosidase (MOGS))
    抗原表位
    • 15
    • 10
    • 8
    • 7
    • 7
    • 1
    • 1
    C-Term
    适用
    • 52
    • 13
    • 4
    • 2
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    人, 小鼠
    宿主
    • 53
    克隆类型
    • 53
    多克隆
    标记
    • 19
    • 5
    • 5
    • 5
    • 4
    • 4
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This GCS1 antibody is un-conjugated
    应用范围
    • 53
    • 31
    • 13
    • 13
    • 3
    • 3
    • 3
    • 2
    • 2
    • 1
    • 1
    Western Blotting (WB), Enzyme Immunoassay (EIA)
    特异性
    This antibody is specific to GCS1 (C-term).
    纯化方法
    Protein G Chromatography, eluted with high and low pH buffers and neutralized immediately, followed by dialysis against PBS.
    免疫原
    This antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide selected form the C-terminal region of human GCS1.
    亚型
    Ig Fraction
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    Discover our top product MOGS Primary Antibody
  • 应用备注
    ELISA: 1/1,000. Western Blot: 1/100-1/500.
    Other applications not tested.
    Optimal dilutions are dependent on conditions and should be determined by the user.
    限制
    仅限研究用
  • 状态
    Liquid
    浓度
    0.25 mg/mL
    缓冲液
    PBS with 0.09 % (W/V) Sodium Azide as preservative.
    储存液
    Sodium azide
    注意事项
    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    注意事项
    Avoid repeated freezing and thawing.
    储存条件
    4 °C/-20 °C
    储存方法
    Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at-20 °C for longer.
  • 抗原
    GCS1 (MOGS) (Mannosyl-Oligosaccharide Glucosidase (MOGS))
    别名
    MOGS / GCS1 (MOGS 产品)
    别名
    Afu6g04210 antibody, AO090701000141 antibody, Mogs antibody, CDG2B antibody, CWH41 antibody, DER7 antibody, GCS1 antibody, 1810017N02Rik antibody, AI181835 antibody, Gcs1 antibody, gcs1 antibody, im:7160827 antibody, wu:fe50a12 antibody, wu:fk09a10 antibody, zgc:158312 antibody, mannosyl-oligosaccharide glucosidase antibody, mannosyl-oligosaccharide glucosidase GCS1 antibody, mannosyl-oligosaccharide glucosidase L homeolog antibody, mannosyl oligosaccharide glucosidase antibody, glucosidase 1 antibody, AFUA_6G04210 antibody, Tc00.1047053511015.10 antibody, Tc00.1047053511805.10 antibody, LOC5576381 antibody, AOR_1_260114 antibody, MGYG_00305 antibody, TERG_01248 antibody, mogs.L antibody, TTHERM_00636930 antibody, LOAG_03690 antibody, Gcs1 antibody, MOGS antibody, Mogs antibody, mogs antibody
    背景
    GCS1 cleaves the distal alpha 1,2-linked glucose residue from the Glc(3)Man(9)GlcNAc(2) oligosaccharide precursor in a highly specific manner. Defects in GCS1 are the cause of type IIb congenital disorder of glycosylation (CDGIIb). This syndrome is also known as glucosidase I deficiency and is characterized by marked generalized hypotonia and hypomotility of the neonate, dysmorphic features, including a prominent occiput, short palpebral fissures, retrognathia, high arched palate, generalized edema, and hypoplastic genitalia. Symptoms include hepatomegaly, hypoventilation, feeding problems and seizures. The clinical course is progressive and survival is at most a few months.Synonyms: Mannosyl-oligosaccharide glucosidase, Processing A-glucosidase I
    分子量
    91840 Da
    基因ID
    7841, 5874
    UniProt
    Q13724
    途径
    SARS-CoV-2 Protein Interactome
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