GCS1 抗体 (C-Term)
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Quick Overview for GCS1 抗体 (C-Term) (ABIN357670)
抗原
See all GCS1 (MOGS) 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- C-Term
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特异性
- This antibody is specific to GCS1 (C-term).
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纯化方法
- Protein G Chromatography, eluted with high and low pH buffers and neutralized immediately, followed by dialysis against PBS.
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免疫原
- This antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide selected form the C-terminal region of human GCS1.
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亚型
- Ig Fraction
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anti-Mannosyl-Oligosaccharide Glucosidase (MOGS) (AA 60-320) antibody
MOGS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Mannosyl-Oligosaccharide Glucosidase (MOGS) antibodyMOGS 适用: 人, 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
anti-Mannosyl-Oligosaccharide Glucosidase (MOGS) (AA 144-193) antibodyMOGS 适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 马, 兔, 斑马鱼, Bat, 猴, Pig WB 宿主: 兔 Polyclonal unconjugated
anti-Mannosyl-Oligosaccharide Glucosidase (MOGS) antibodyMOGS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Mannosyl-Oligosaccharide Glucosidase (MOGS) (N-Term) antibodyMOGS 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
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ELISA: 1/1,000. Western Blot: 1/100-1/500.
Other applications not tested.
Optimal dilutions are dependent on conditions and should be determined by the user. -
限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.25 mg/mL
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缓冲液
- PBS with 0.09 % (W/V) Sodium Azide as preservative.
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储存液
- Sodium azide
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注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- Avoid repeated freezing and thawing.
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储存条件
- 4 °C/-20 °C
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储存方法
- Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at-20 °C for longer.
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- GCS1 (MOGS) (Mannosyl-Oligosaccharide Glucosidase (MOGS))
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别名
- MOGS / GCS1
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背景
- GCS1 cleaves the distal alpha 1,2-linked glucose residue from the Glc(3)Man(9)GlcNAc(2) oligosaccharide precursor in a highly specific manner. Defects in GCS1 are the cause of type IIb congenital disorder of glycosylation (CDGIIb). This syndrome is also known as glucosidase I deficiency and is characterized by marked generalized hypotonia and hypomotility of the neonate, dysmorphic features, including a prominent occiput, short palpebral fissures, retrognathia, high arched palate, generalized edema, and hypoplastic genitalia. Symptoms include hepatomegaly, hypoventilation, feeding problems and seizures. The clinical course is progressive and survival is at most a few months.Synonyms: Mannosyl-oligosaccharide glucosidase, Processing A-glucosidase I
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分子量
- 91840 Da
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基因ID
- 7841, 5874
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UniProt
- Q13724
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途径
- SARS-CoV-2 Protein Interactome
抗原
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