Arylsulfatase A 抗体 (AA 210-509)
Quick Overview for Arylsulfatase A 抗体 (AA 210-509) (ABIN3022463)
抗原
See all Arylsulfatase A (ARSA) 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 210-509
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序列
- LMADAQRQDR PFFLYYASHH THYPQFSGQS FAERSGRGPF GDSLMELDAA VGTLMTAIGD LGLLEETLVI FTADNGPETM RMSRGGCSGL LRCGKGTTYE GGVREPALAF WPGHIAPGVT HELASSLDLL PTLAALAGAP LPNVTLDGFD LSPLLLGTGK SPRQSLFFYP SYPDEVRGVF AVRTGKYKAH FFTQGSAHSD TTADPACHAS SSLTAHEPPL LYDLSKDPGE NYNLLGGVAG ATPEVLQALK QLQLLKAQLD AAVTFGPSQV ARGEDPALQI CCHPGCTPRP ACCHCPDPHA
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交叉反应
- 人, 小鼠
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产品特性
- Polyclonal Antibodies
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纯化方法
- Affinity purification
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免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 210-509 of human ARSA (NP_000478.3).
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亚型
- IgG
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应用备注
- WB,1:500 - 1:2000
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- Avoid freeze / thaw cycles
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- Arylsulfatase A (ARSA)
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别名
- ARSA
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背景
- The protein encoded by this gene hydrolyzes cerebroside sulfate to cerebroside and sulfate. Defects in this gene lead to metachromatic leucodystrophy (MLD), a progressive demyelination disease which results in a variety of neurological symptoms and ultimately death. Alternatively spliced transcript variants have been described for this gene.,ARSA,MLD,Cancer,Signal Transduction,Cell Biology & Developmental Biology,Autophagy,Endocrine & Metabolism,Neuroscience,Neurodegenerative Diseases,ARSA
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分子量
- 44 kDa/53 kDa
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基因ID
- 410
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UniProt
- P15289
抗原
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