GALNS 抗体 (Center)
Quick Overview for GALNS 抗体 (Center) (ABIN2856743)
抗原
See all GALNS 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- Center
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产品特性
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Rabbit Polyclonal antibody to GALNS (galactosamine (N-acetyl)-6-sulfate sulfatase)
GALNS antibody -
纯化方法
- Purified by antigen-affinity chromatography.
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免疫原
- Recombinant protein encompassing a sequence within the center region of human GALNS. The exact sequence is proprietary.
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亚型
- IgG
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anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 181-289) antibody
GALNS 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 1-522) antibodyGALNS 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 353-522) antibodyGALNS 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 236-263) antibodyGALNS 适用: 人 WB, IF, IHC (p), FACS 宿主: 兔 Polyclonal RB31386 unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 243-271), (Middle Region) antibodyGALNS 适用: 人 WB, IF, IHC (p), FACS, EIA 宿主: 兔 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 172-381) antibodyGALNS 适用: 大鼠 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 168-377) antibodyGALNS 适用: 小鼠 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (Internal Region) antibodyVerified GALNS 适用: 人 WB, ELISA 宿主: 山羊 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) (AA 1-522) antibodyGALNS 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) antibody (FITC)GALNS 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal FITC
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应用备注
- Suggested dilution Reference ICC/IF 1:100-1:1000* IHC (Formalin-fixed paraffin-embedded sections) 1:100-1:1000* Western blot 1:500-1:3000* Not tested in other applications. *Optimal dilutions/concentrations should be determined by the researcher.Suggested dilutionReferenceICC/IF1:100-1:1000* IHC (Formalin-fixed paraffin-embedded sections)1:100-1:1000* Western blot1:500-1:3000*
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说明
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Positive Control: H1299 , Neuro2A , C2C12 , PC-12 , Rat2
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 mg/mL
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缓冲液
- 0.1M Tris, 0.1M Glycine, 10 % Glycerol ( pH 7). 0.01 % Thimerosal was added as a preservative.
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储存液
- Thimerosal (Merthiolate)
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注意事项
- This product contains Thimerosal (Merthiolate): a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Keep as concentrated solution. Aliquot and store at -20°C or below. Avoid multiple freeze-thaw cycles.
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- GALNS (Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS))
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别名
- GALNS
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背景
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This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.
Cellular Localization: Lysosome -
分子量
- 58 kDa
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基因ID
- 2588
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途径
- Glycosaminoglycan Metabolic Process
抗原
-
