SGSH 抗体
Quick Overview for SGSH 抗体 (ABIN2854346)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
-
-
交叉反应
- 人
-
产品特性
-
Rabbit polyclonal antibody to SGSH (N-sulfoglucosamine sulfohydrolase)
SGSH antibody [N1N3] -
纯化方法
- Affinity purified by Protein A.
-
免疫原
- Recombinant protein encompassing a sequence within the center region of human SGSH. The exact sequence is proprietary.
-
亚型
- IgG
-
-
-
-
应用备注
- WB: 1:500-1:3000. Optimal dilutions/concentrations should be determined by the researcher. Not tested in other applications.
-
说明
-
Positive Control: 293T
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
浓度
- 2 mg/mL
-
缓冲液
- 1XPBS ( pH 7), 40 % Glycerol, 0.01 % Thimerosal
-
储存液
- Thimerosal (Merthiolate)
-
注意事项
- This product contains Thimerosal (Merthiolate): a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
储存条件
- 4 °C,-20 °C
-
储存方法
- Store as concentrated solution. Centrifuge briefly prior to opening vial. For short-term storage (1-2 weeks), store at 4°C. For long-term storage, aliquot and store at -20°C or below. Avoid multiple freeze-thaw cycles.
-
-
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
-
别名
- N-sulfoglucosamine sulfohydrolase
-
背景
-
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Cellular Localization: Lysosome -
分子量
- 57 kDa
-
基因ID
- 6448
-
UniProt
- P51688
-
途径
- Glycosaminoglycan Metabolic Process
抗原
-