HMBS 抗体 (Middle Region)
(1 reference)-
- 抗原 See all HMBS 抗体
- HMBS (Hydroxymethylbilane Synthase (HMBS))
-
抗原表位
- Middle Region
-
适用
- 人, 小鼠, 大鼠, 兔, 犬, 马, 豚鼠, Cow, 斑马鱼, 绵羊, 山羊
-
宿主
- 兔
-
克隆类型
- 多克隆
-
标记
- This HMBS antibody is un-conjugated
-
应用范围
- Western Blotting (WB)
- 序列
- SSLRRAAQLQ RKFPHLEFRS IRGNLNTRLR KLDEQQEFSA IILATAGLQR
- 预测反应
- Cow: 93%, Dog: 93%, Goat: 93%, Guinea Pig: 100%, Horse: 93%, Human: 100%, Mouse: 93%, Rabbit: 100%, Rat: 100%, Sheep: 93%, Zebrafish: 91%
- 产品特性
- This is a rabbit polyclonal antibody against HMBS. It was validated on Western Blot using a cell lysate as a positive control.
- 纯化方法
- Affinity Purified
- 免疫原
- The immunogen is a synthetic peptide directed towards the middle region of human HMBS
- Top Product
- Discover our top product HMBS Primary Antibody
-
anti-Hydroxymethylbilane Synthase (HMBS) (AA 283-330) antibody
HMBS 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibodyHMBS 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibodyHMBS 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 3E8 unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 85-337) antibodyHMBS 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (Internal Region) antibodyHMBS 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 160-173) antibodyVerified HMBS 适用: 人 WB, ELISA, IHC 宿主: 山羊 Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibodyHMBS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) antibodyHMBS 适用: 人 WB 宿主: 兔 Monoclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) antibodyHMBS 适用: 人, 小鼠, 大鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) antibodyHMBS 适用: 人, 小鼠, 大鼠 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
-
- 应用备注
- Optimal working dilutions should be determined experimentally by the investigator.
- 说明
-
Antigen size: 361 AA
- 限制
- 仅限研究用
-
- 状态
- Liquid
- 浓度
- Lot specific
- 缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 注意事项
- Avoid repeated freeze-thaw cycles.
- 储存条件
- -20 °C
- 储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
-
-
: "Acute intermittent porphyria with peripheral neuropathy: a follow-up study after hematin treatment." in: Journal of the neurological sciences, Vol. 260, Issue 1-2, pp. 231-5, (2007) (PubMed).
-
: "Acute intermittent porphyria with peripheral neuropathy: a follow-up study after hematin treatment." in: Journal of the neurological sciences, Vol. 260, Issue 1-2, pp. 231-5, (2007) (PubMed).
-
- 抗原
- HMBS (Hydroxymethylbilane Synthase (HMBS))
- 别名
- HMBS (HMBS 产品)
- 别名
- PBG-D antibody, PBGD antibody, PORC antibody, UPS antibody, URO-S antibody, hemC antibody, pbg-d antibody, pbgd antibody, ups antibody, SPAC806.01 antibody, DDBDRAFT_0186148 antibody, DDBDRAFT_0231417 antibody, DDB_0186148 antibody, DDB_0231417 antibody, Hmbs antibody, NV50236 antibody, T25658 antibody, Ups antibody, Uros1 antibody, hmbs antibody, zgc:64128 antibody, hmbsl antibody, id:ibd5004 antibody, im:7140060 antibody, zgc:110690 antibody, hydroxymethylbilane synthase antibody, hydroxymethylbilane synthase S homeolog antibody, hydroxymethylbilane synthase L homeolog antibody, hydroxymethylbilane synthase (predicted) antibody, Hydroxymethylbilane synthase antibody, hydroxymethylbilane synthase a antibody, hydroxymethylbilane synthase, b antibody, HMBS antibody, Hmbs antibody, hmbs antibody, hmbs.2.S antibody, hmbs.L antibody, CNC02250 antibody, hem3 antibody, hemC antibody, Trad_0335 antibody, Plabr_2100 antibody, Sgly_3113 antibody, SMLT_RS19660 antibody, PMI_RS16580 antibody, hmbsa antibody, hmbsb antibody
- 背景
-
HMBS is a member of the hydroxymethylbilane synthase superfamily. It is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria.This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.
Alias Symbols: PBG-D, PBGD, UPS, PORC
Protein Interaction Partner: RANBP9, APP, UBC,
Protein Size: 361 - 分子量
- 40 kDa
- 基因ID
- 3145
- NCBI登录号
- NM_000190, NP_000181
- UniProt
- P08397
-
