SGSH 抗体 (C-Term)
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北京 101111
Quick Overview for SGSH 抗体 (C-Term) (ABIN2783228)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- C-Term
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原理
- SGSH Antibody - C-terminal region
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序列
- ARWELYDRSR DPHETQNLAT DPRFAQLLEM LRDQLAKWQW ETHDPWVCAP
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预测反应
- Cow: 79%, Dog: 86%, Horse: 93%, Human: 100%, Mouse: 79%, Rat: 79%
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产品特性
- This is a rabbit polyclonal antibody against SGSH. It was validated on Western Blot.
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纯化方法
- Affinity Purified
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免疫原
- The immunogen is a synthetic peptide directed towards the C-terminal region of human SGSH
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应用备注
- Optimal working dilution should be determined by the investigator.
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说明
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We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP48124-100UG
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.5 mg/mL
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缓冲液
- Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- prevent freeze-thaw cycles
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储存条件
- 4 °C,-20 °C
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储存方法
- For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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别名
- SGSH
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背景
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Background Information: This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Gene Name: N-sulfoglucosamine sulfohydrolase
Alternative Symbols: HSS, SFMD, MPS3A
Protein Name: N-sulphoglucosamine sulphohydrolase
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分子量
- 32kDa
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基因ID
- 6448
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NCBI登录号
- NP_000190
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UniProt
- P51688
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途径
- Glycosaminoglycan Metabolic Process
抗原
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