PCCA 抗体 (N-Term)
(1 reference)Quick Overview for PCCA 抗体 (N-Term) (ABIN2777736)
抗原
See all PCCA 抗体适用
宿主
克隆类型
标记
应用范围
-
-
抗原表位
- N-Term
-
序列
- LYYSRQCLMV SRNLGSVGYD PNEKTFDKIL VANRGEIACR VIRTCKKMGI
-
预测反应
- Cow: 86%, Dog: 86%, Horse: 83%, Human: 100%, Mouse: 77%, Pig: 86%, Rabbit: 86%, Rat: 86%, Zebrafish: 75%
-
产品特性
- This is a rabbit polyclonal antibody against PCCA. It was validated on Western Blot using a cell lysate as a positive control.
-
纯化方法
- Affinity Purified
-
免疫原
- The immunogen is a synthetic peptide directed towards the N terminal region of human PCCA
-
-
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (AA 362-390) antibody
PCCA 适用: 人, 大鼠 WB, IHC (p) 宿主: 兔 Polyclonal RB31944 unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (AA 1-703) antibodyPCCA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (AA 585-720) antibodyPCCA 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (C-Term) antibodyPCCA 适用: 人, 小鼠 WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (AA 580-728) antibodyPCCA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (AA 38-87) antibodyPCCA 适用: 人, 小鼠, Cow, 马, 斑马鱼, 兔 WB 宿主: 兔 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) antibodyPCCA 适用: 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (AA 678-728) antibodyPCCA 适用: 人, 小鼠, 大鼠, Cow, 马, 斑马鱼, 犬, Pig, 小鸡 WB, IHC, IHC (p), IF 宿主: 兔 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (AA 449-728) antibodyPCCA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Propionyl CoA Carboxylase, alpha Polypeptide (PCCA) (N-Term) antibodyPCCA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
-
-
应用备注
- Optimal working dilutions should be determined experimentally by the investigator.
-
说明
-
Antigen size: 728 AA
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
浓度
- Lot specific
-
缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
-
储存液
- Sodium azide
-
注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
注意事项
- Avoid repeated freeze-thaw cycles.
-
储存条件
- -20 °C
-
储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
-
-
-
: "Propionic and methylmalonic acidemia: antisense therapeutics for intronic variations causing aberrantly spliced messenger RNA." in: American journal of human genetics, Vol. 81, Issue 6, pp. 1262-70, (2011) (PubMed).
-
: "Propionic and methylmalonic acidemia: antisense therapeutics for intronic variations causing aberrantly spliced messenger RNA." in: American journal of human genetics, Vol. 81, Issue 6, pp. 1262-70, (2011) (PubMed).
-
- PCCA (Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))
-
别名
- PCCA
-
背景
-
PCCA is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA is the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia.The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Two transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: -
Protein Interaction Partner: HUWE1, PARK2, IFIT1, UBE2N, UBC, EBNA-LP, PCCB,
Protein Size: 728 -
分子量
- 75 kDa
-
基因ID
- 5095
-
NCBI登录号
- NM_000282, NP_000273
-
UniProt
- Q8WXQ7
-
途径
- Monocarboxylic Acid Catabolic Process
抗原
-
