SGSH 抗体 (AA 44-200)
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北京 101111
Quick Overview for SGSH 抗体 (AA 44-200) (ABIN1886470)
抗原
See all SGSH 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 44-200
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纯化方法
- Affinity purified by Protein A.
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免疫原
- Recombinant protein fragment contain a sequence corresponding to a region within amino acids 44 and 200 of Human SGSH
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应用备注
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Suggested dilutions:
Western blotting: 1.500-1.3000 -
限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- 0.1 M Tris-buffered saline with 10 % Glycerol (pH 7.0).0.01 % Thimerosal was added as a preservative.
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储存液
- Thimerosal (Merthiolate)
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注意事项
- Biohazard Informations: This product contains thimerosal which is hazardous.
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储存条件
- 4 °C/-20 °C
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储存方法
- Store at -20 °C for long term preservation (recommended). Store at 4 °C for short term use.
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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别名
- SGSH
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背景
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This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate.Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate.Transcripts of varying sizes have been reported but their biological validity has not been determined.[provided by RefSeq]
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分子量
- 57 kDa
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基因ID
- 6448
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NCBI登录号
- NM_000199, NP_000190
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途径
- Glycosaminoglycan Metabolic Process
抗原
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