GALNS 抗体 (AA 20-269)
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北京 101111
Quick Overview for GALNS 抗体 (AA 20-269) (ABIN1886170)
抗原
See all GALNS 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 20-269
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纯化方法
- Purified by antigen-affinity chromatography.
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免疫原
- Recombinant protein fragment contain a sequence corresponding to a region within amino acids 20 and 269 of GALNS
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应用备注
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Suggested dilutions:
Western blotting: 1.500-1.3000
Immunohistochemistry: 1.100-1.500
Immunofluorescence: 1.100-1.200 -
限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- 0.1 M Tris-buffered saline with 10 % Glycerol (pH 7.0).0.01 % Thimerosal was added as a preservative.
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储存液
- Thimerosal (Merthiolate)
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注意事项
- Biohazard Informations: This product contains thimerosal which is hazardous.
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储存条件
- 4 °C/-20 °C
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储存方法
- Store at -20 °C for long term preservation (recommended). Store at 4 °C for short term use.
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- GALNS (Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS))
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别名
- GALNS
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背景
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This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate.Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme.Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.[provided by RefSeq]
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分子量
- 58 kDa
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基因ID
- 2588
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NCBI登录号
- NP_000503, NM_000512
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途径
- Glycosaminoglycan Metabolic Process
抗原
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