CTNS 抗体 (C-Term)
(5 references)Our Local Distributor
北京 101111
Quick Overview for CTNS 抗体 (C-Term) (ABIN1881240)
抗原
See all CTNS 抗体适用
宿主
克隆类型
标记
应用范围
克隆位点
-
-
抗原表位
- AA 341-367, C-Term
-
纯化方法
- This antibody is purified through a protein A column, followed by peptide affinity purification.
-
免疫原
- This CTNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 341-367 amino acids from the C-terminal region of human CTNS.
-
亚型
- Ig Fraction
-
-
anti-Cystinosis, Nephropathic (CTNS) (AA 1-100) antibody
CTNS 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 5G6 unconjugated
anti-Cystinosis, Nephropathic (CTNS) (AA 1-400) antibodyCTNS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Cystinosis, Nephropathic (CTNS) (AA 1-100) antibodyCTNS 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
anti-Cystinosis, Nephropathic (CTNS) (AA 1-100) antibodyCTNS 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC, IHC (p) 宿主: 小鼠 Monoclonal 5G6 unconjugated
anti-Cystinosis, Nephropathic (CTNS) antibodyCTNS 适用: 人, 小鼠, 大鼠 IF 宿主: 兔 Polyclonal unconjugated
-
-
应用备注
- WB: 1:1000
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
缓冲液
- Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
-
储存液
- Sodium azide
-
注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
储存条件
- 4 °C,-20 °C
-
有效期
- 6 months
-
-
-
: "Analysis of CTNS gene transcripts in nephropathic cystinosis." in: Pediatric nephrology (Berlin, Germany), Vol. 25, Issue 7, pp. 1263-7, (2010) (PubMed).
: "A futile cycle, formed between two ATP-dependant gamma-glutamyl cycle enzymes, gamma-glutamyl cysteine synthetase and 5-oxoprolinase: the cause of cellular ATP depletion in nephrotic cystinosis?" in: Journal of biosciences, Vol. 35, Issue 1, pp. 21-5, (2010) (PubMed).
: "Modulation of CTNS gene expression by intracellular thiols." in: Free radical biology & medicine, Vol. 48, Issue 7, pp. 865-72, (2010) (PubMed).
: "Characterization of CTNS mutations in Arab patients with cystinosis." in: Ophthalmic genetics, Vol. 30, Issue 4, pp. 185-9, (2009) (PubMed).
: "Analysis of the CTNS gene in 32 cystinosis patients from Spain." in: Clinical genetics, Vol. 76, Issue 5, pp. 486-9, (2009) (PubMed).
-
: "Analysis of CTNS gene transcripts in nephropathic cystinosis." in: Pediatric nephrology (Berlin, Germany), Vol. 25, Issue 7, pp. 1263-7, (2010) (PubMed).
-
- CTNS (Cystinosis, Nephropathic (CTNS))
-
别名
- CTNS
-
背景
- This gene encodes a seven-transmembrane domain protein that functions to transport cystine out of lysosomes. Its activity is driven by the H+ electrochemical gradient of the lysosomal membrane. Mutations in this gene cause cystinosis, a lysosomal storage disorder. Alternative splicing results in multiple transcript variants.
-
分子量
- 41738
-
NCBI登录号
- NP_001026851, NP_004928
-
UniProt
- O60931
抗原
-
