FKRP 抗体 (AA 1-50)
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北京 101111
Quick Overview for FKRP 抗体 (AA 1-50) (ABIN1534132)
抗原
See all FKRP 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 1-50
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原理
- FKRP Antibody
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特异性
- FKRP Polyclonal Antibody detects endogenous levels of FKRP protein.
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纯化方法
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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纯度
- > 95 %
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免疫原
- The antiserum was produced against synthesized peptide derived from human FKRP. AA range:1-50
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亚型
- IgG
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应用备注
- WB 1:500 - 1:2000. IF 1:200 - 1:1000. ELISA: 1:20000. Not yet tested in other applications.
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 mg/mL
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缓冲液
- Liquid in PBS containing 50 % glycerol, 0.5 % BSA and 0.02 % sodium azide.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C/1 year
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有效期
- 12 months
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- FKRP (Fukutin Related Protein (FKRP))
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别名
- FKRP
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背景
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Synonyms: FKRP, Fukutin-related protein
Background: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008],
Gene Name: FKRP
Protein Name: Fukutin-related protein
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分子量
- 54 kDa
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基因ID
- 79147
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OMIM
- 236670
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UniProt
- Q9H9S5
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途径
- Regulation of Carbohydrate Metabolic Process
抗原
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