ALG8 抗体
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北京 101111
Quick Overview for ALG8 抗体 (ABIN1449889)
抗原
See all ALG8 抗体适用
宿主
克隆类型
标记
应用范围
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序列
- LELKLLDPSQ IPRASMTSGL VQQSQHTVLP SVSPSATLIC TLIAILPSVF
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交叉反应 （详细）
- Species reactivity (expected):Mouse, Human, Chicken, Dog, Bovine, PigSpecies reactivity (tested):Human
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纯化方法
- Purified using peptide immunoaffinity column
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免疫原
- Synthetic peptide corresponding to a region of Rat ALG8
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anti-Asparagine-Linked Glycosylation 8, alpha-1,3-Glucosyltransferase Homolog (ALG8) antibody
ALG8 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Asparagine-Linked Glycosylation 8, alpha-1,3-Glucosyltransferase Homolog (ALG8) (AA 260-334) antibodyALG8 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 2E10 unconjugated
anti-Asparagine-Linked Glycosylation 8, alpha-1,3-Glucosyltransferase Homolog (ALG8) (AA 301-350) antibodyALG8 适用: 人, 小鼠, Cow, 犬, Pig, 大鼠, 马, 兔, 斑马鱼, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- Optimal working dilution should be determined by the investigator.
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限制
- 仅限研究用
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溶解方式
- Add 50 μL of distilled water to a final concentration of 1 mg/mL.
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注意事项
- Avoid repeated freezing and thawing.
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储存条件
- 4 °C/-20 °C
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储存方法
- Store lyophilized at 2-8 °C or at -20 °C long term. After reconstitution store the antibody undiluted at 2-8 °C for up to one month or in aliquots at -20 °C long term.
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- ALG8 (Asparagine-Linked Glycosylation 8, alpha-1,3-Glucosyltransferase Homolog (ALG8))
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别名
- ALG8
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背景
- ALG8 adds the second glucose residue to the lipid-linked oligosaccharide precursor for N-linked glycosylation and transfers glucose from dolichyl phosphate glucose (Dol-P-Glc) onto the lipid-linked oligosaccharide Glc1Man9GlcNAc(2)-PP-Dol. Defects in ALG8 are the cause of congenital disorder of glycosylation type 1H (CDG1H). CDGs are a family of severe inherited diseases caused by a defect in protein N-glycosylation. They are characterized by under-glycosylated serum proteins. These multisystem disorders present with a wide variety of clinical features, such as disorders of the nervous system development, psychomotor retardation, dysmorphic features, hypotonia, coagulation disorders, and immunodeficiency. The broad spectrum of features reflects the critical role of N-glycoproteins during embryonic development, differentiation, and maintenance of cell functions.Synonyms: 3-glucosyltransferase, Asparagine-linked glycosylation protein 8, Dolichyl-P-Glc:Glc1Man9GlcNAc2-PP-dolichyl glucosyltransferase, HUSSY-02, Probable dolichyl pyrophosphate Glc1Man9GlcNAc2 alpha-1
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基因ID
- 293129
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NCBI登录号
- NP_001029299
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途径
- SARS-CoV-2 Protein Interactome
抗原
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