T-Box 1 抗体 (AA 165-270) (AbBy Fluor® 488)
Quick Overview for T-Box 1 抗体 (AA 165-270) (AbBy Fluor® 488) (ABIN1398106)
抗原
See all T-Box 1 (TBX1) 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 165-270
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交叉反应
- 人, 小鼠, 大鼠
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预测反应
- Dog,Cow,Pig,Horse,Chicken
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纯化方法
- Purified by Protein A.
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免疫原
- KLH conjugated synthetic peptide derived from human TBX1
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亚型
- IgG
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anti-T-Box 1 (TBX1) (AA 327-356), (C-Term) antibody
TBX1 适用: 人 WB, IF, IHC (p) 宿主: 兔 Polyclonal RB22154 unconjugated
anti-T-Box 1 (TBX1) (C-Term) antibodyTBX1 适用: 人 WB, ELISA, IF 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) antibodyTBX1 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) (C-Term) antibodyTBX1 适用: 人 WB, ELISA, IF, ICC 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) (AA 396-445) antibodyTBX1 适用: 人, 小鼠, 大鼠, 豚鼠, 兔, 犬 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) (C-Term) antibodyTBX1 适用: 人 WB, IHC, IF, IC 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) (C-Term) antibodyTBX1 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) (AA 22-107) antibodyTBX1 适用: 人 ELISA, IF 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) (AA 327-356) antibodyTBX1 适用: 人 WB, IHC, IF, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-T-Box 1 (TBX1) (AA 324-373) antibodyTBX1 适用: 人, 小鼠, 大鼠, 豚鼠, 兔 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- FCM 1:20-100
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 μg/μL
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缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
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储存液
- ProClin
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注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
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有效期
- 12 months
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- T-Box 1 (TBX1)
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别名
- TBX1
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背景
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Synonyms: Brachyury, CAFS, CTHM, DGCR, DGS, DORV, T box 1, T box 1 transcription factor, T box 1 transcription factor C, T box, T box protein 1, T box transcription factor TBX 1, T box transcription factor TBX1, T-box 1, T-box protein 1, T-box transcription factor TBX1, TBX 1, TBX 1C, tbx1, TBX1_HUMAN, TBX1C, Testis specic T box protein, Testis-specic T-box protein, TGA, VCFS.
Background: Probable transcriptional regulator involved in developmental processes. Is required for normal development of the pharyngeal arch arteries.Involvement in disease:Haploinsufficiency of the TBX1 gene is responsible for most of the physical malformations present in DiGeorge syndrome (DGS) and velocardiofacial syndrome (VCFS) . DGS is characterized by the association of several malformations: hypoplastic thymus and parathyroid glands, congenital conotruncal cardiopathy, and a subtle but characteristic facial dysmorphology. VCFS is marked by the association of congenital conotruncal heart defects, cleft palate or velar insufficiency, facial dysmorpholgy and learning difficulties. It is now accepted that these two syndromes represent two forms of clinical expression of the same entity manifesting at different stages of life.Defects in TBX1 are a cause of DiGeorge syndrome (DGS) .Defects in TBX1 are a cause of velocardiofacial syndrome (VCFS) .Defects in TBX1 are a cause of conotruncal heart malformations (CTHM). CTHM consist of cardiac outflow tract defects, such as tetralogy of Fallot, pulmonary atresia, double-outlet right ventricle, truncus arteriosus communis, and aortic arch anomalies.
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基因ID
- 6899
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途径
- Retinoic Acid Receptor Signaling Pathway, Sensory Perception of Sound, Cellular Response to Molecule of Bacterial Origin, Regulation of Muscle Cell Differentiation
抗原
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