GBA 抗体
Quick Overview for GBA 抗体 (ABIN1387836)
抗原
See all GBA 抗体适用
宿主
克隆类型
标记
应用范围
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纯化方法
- Purified by Protein A.
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免疫原
- KLH conjugated synthetic peptide derived from human Acid beta-glucosidase
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亚型
- IgG
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anti-Glucosidase, Beta, Acid (GBA) (AA 146-235) antibody
GBA 适用: 人 WB, ELISA, IHC (p), IF 宿主: 小鼠 Monoclonal 2E2 unconjugated
anti-Glucosidase, Beta, Acid (GBA) (AA 117-214) antibodyGBA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Beta, Acid (GBA) antibodyGBA 适用: 小鼠, 大鼠 IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Beta, Acid (GBA) (AA 334-498) antibodyGBA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Beta, Acid (GBA) antibodyGBA 适用: 人, 小鼠 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Beta, Acid (GBA) (C-Term) antibodyGBA 适用: 人 WB, ICC, IHC (p), IF 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Beta, Acid (GBA) (AA 255-509) antibodyGBA 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Beta, Acid (GBA) (AA 215-343) antibodyGBA 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Beta, Acid (GBA) (AA 146-235) antibodyGBA 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 2H4 unconjugated
anti-Glucosidase, Beta, Acid (GBA) (AA 1-536) antibodyGBA 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
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应用备注
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WB 1:100-1000
IHC-P 1:100-500
IF(IHC-P) 1:50-200 -
限制
- 仅限研究用
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状态
- Liquid
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浓度
- 1 μg/μL
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缓冲液
- Aqueous buffered solution containing 1 % BSA, 50 % glycerol and 0.09 % sodium azide.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C
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有效期
- 12 months
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- GBA (Glucosidase, Beta, Acid (GBA))
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别名
- GBA/Acid beta-Glucosidase
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背景
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Beta-Glucosidase is a predominantly liver enzyme which efficiently hydrolyzes Beta-D-glucoside and Beta-D-galactoside. Defects in Beta-Glucosidase cause Gaucher disease, an inherited condition distinguished by the accumulation of glucosylceramide within the cells of the reticuloendothelial system. Beta-Glucosidase is used in enzyme replacement treatment aimed at treating Gaucher disease. The absorption of dietary flavonoid glycosides in humans involves a critical deglycosylation step that is mediated by epithelial Beta-glucosidases.
Synonyms: Acid beta glucosidase, Acid beta-glucosidase, Alglucerase, Beta glucocerebrosidase, BETA GLUCOSIDASE, ACID, Beta-glucocerebrosidase, betaGC, D glucosyl N acylsphingosine glucohydrolase, D-glucosyl-N-acylsphingosine glucohydrolase, EC 3.2.1.45 , GBA, Gba protein, GBA1, GC antibody GCase, GCB, GLCM_HUMAN, GLUC, Glucocerebrosidase alt., Glucocerebrosidase, GLUCOCEREBROSIDASE PSEUDOGENE, Glucosidase beta, Glucosidase, beta, acid, Glucosidase, beta, acid includes glucosylceramidase, Glucosylceramidase, Imiglucerase, Lysosomal glucocerebrosidase.
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途径
- Cellular Glucan Metabolic Process
抗原
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