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SGSH 抗体 (AA 301-388)

Name: SGSH 抗体 (AA 301-388)
SKU: ABIN1386573
Availability: OutOfStock

This anti-SGSH antibody is a 兔多克隆 antibody detecting SGSH in WB, ELISA, ICC, IF (cc), IF (p), IHC (p) 和 IHC (fro). Suitable for 大鼠.

Raji cell lysates probed with Anti-SGSH/Sulphamidase Polyclonal Antibody, Unconjugated (ABIN1386573) at 1:300 in 4˚C. (SGSH 抗体 (AA 301-388))

1 image

产品编号 ABIN1386573

发货至: 中国

Quick Overview for SGSH 抗体 (AA 301-388) (ABIN1386573)

抗原

See all SGSH 抗体

SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

适用

大鼠

宿主

兔

克隆类型

多克隆

标记

This SGSH antibody is un-conjugated

应用范围

Western Blotting (WB), ELISA, Immunocytochemistry (ICC), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Immunohistochemistry (Frozen Sections) (IHC (fro))

Discover our top product SGSH Primary Antibody

抗原表位
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AA 301-388

交叉反应

大鼠

预测反应

Human,Mouse,Dog

纯化方法

Purified by Protein A.

免疫原

KLH conjugated synthetic peptide derived from human Sulphamidase

亚型

IgG
anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 21-389) antibody
SGSH 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibody
SGSH 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibody
SGSH 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (C-Term) antibody
SGSH 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 1-502) antibody
SGSH 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 44-200) antibody
SGSH 适用: 人 WB 宿主: 兔 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 273-502) antibody
SGSH 适用: 人 WB 宿主: 兔 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (N-Term) antibody
SGSH 适用: 人, 大鼠, 小鼠, Cow, 马, 犬, Pig, 豚鼠 WB 宿主: 兔 Polyclonal unconjugated

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 301-388) antibody (AbBy Fluor® 555)
SGSH 适用: 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555

anti-N-Sulfoglucosamine Sulfohydrolase (SGSH) (AA 301-388) antibody (AbBy Fluor® 488)
SGSH 适用: 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488

应用备注

WB 1:300-5000
ELISA 1:500-1000
IHC-P 1:200-400
IHC-F 1:100-500
IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200
ICC 1:100-500

限制

仅限研究用
状态

Liquid

浓度

1 μg/μL

缓冲液

0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.

储存液

ProClin

注意事项

This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

储存条件

4 °C,-20 °C

储存方法

Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.

有效期

12 months
抗原

SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

别名

SGSH/Sulphamidase

背景

Synonyms: HSS, SFMD, MPS3A, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase, Sulphamidase, SGSH
Background: Sulfatases are enzymes that hydrolyse a diverse range of sulfate esters. Deficiency of lysosomal sulfatases leads to human diseases characterized by the accumulation of either GAGs (glycosaminoglycans) or sulfolipids. Sulfamidase, also known as HSS, SFMD, MPS3A or SGSH, is a 502 amino acid lysosome that belongs to the sulfatase family. It has been suggested that sulfamidase may be involved in the lysosomal degradation of heparan sulfate. Defects in the gene encoding sulfamidase are the cause of Sanfilippo syndrome A, an autosomal recessive lysosomal storage disease caused by impaired degradation of heparan sulfate. Sanfilippo syndrome A is characterized by severe central nervous system degeneration but relatively mild somatic manifestations.

基因ID

6448

UniProt

P51688

途径

Glycosaminoglycan Metabolic Process