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ACADVL 抗体

(Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL))
The protein encoded by this gene is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. This acyl-Coenzyme A dehydrogenase is specific to long-chain and very-long-chain fatty acids. A deficiency in this gene product reduces myocardial fatty acid beta-oxidation and is associated with cardiomyopathy. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Jul 2008].

48 results

ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN881022
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488
产品编号 ABIN881020
 
ACADVL 适用: 人 ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal HRP
产品编号 ABIN708455
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal FITC
产品编号 ABIN708453
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal Cy7
产品编号 ABIN708452
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5.5
产品编号 ABIN708451
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5
产品编号 ABIN708450
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal Cy3
产品编号 ABIN708449
 
ACADVL 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7175436
 
ACADVL 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7175435
 
ACADVL 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7175434
 
ACADVL 适用: 人 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7634037
 
ACADVL 适用: 人, 大鼠, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7111265
 
ACADVL 适用: 人, 小鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6390177
 
KO Validated ACADVL 适用: 人 WB, IF, IHC (p), ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7464798
 
ACADVL 适用: 人, 大鼠, 小鼠 WB, IHC, IF, ICC, IP, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN4886415
 
ACADVL 适用: 人, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5647680
 
ACADVL 适用: 人 WB, IHC, IP 宿主: 兔 Monoclonal 32A31 unconjugated
产品编号 ABIN7603874
 
ACADVL 适用: 人, 大鼠, 小鼠 WB, ELISA, IHC, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5702030
 
ACADVL 适用: 人 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7610508
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (IHC)
    • Immunofluorescence (IF)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunoprecipitation (IP)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Flow Cytometry (FACS)
  • 适用
    • Human
    • Rat
    • Mouse
    • Cow
    • Dog
    • Horse
    • Rabbit
    • Zebrafish (Danio rerio)
    • Guinea Pig
    • Pig
    • Bat
    • Hamster
  • 论文引用
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Goat
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 32A31
    • 5D3
  • 抗原表位
    • AA 251-350
    • AA 403-497
    • C-Term
    • N-Term
    • AA 345-434
    • AA 538-576
    • AA 1-140
    • AA 38-87
    • AA 408-655
    • AA 471-520
    • AA 551-600
    • Internal Region
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • HRP
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • IgG2b
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • Verified
    • KO Validated
  • Supplier
    • antibodies-online
    • Signalway
    • Aviva Systems Biology
    • Biomatik
    • Boster Bio
    • Abbexa
    • NSJ Bioreagents
    • Wuhan Fine biotech

Latest Publications for our ACADVL 抗体

Nouws, Te Brinke, Nijtmans, Houten: "ACAD9, a complex I assembly factor with a moonlighting function in fatty acid oxidation deficiencies." in: Human molecular genetics, Vol. 23, Issue 5, pp. 1311-9, (2014) (PubMed).

De Pauw, Demine, Tejerina, Dieu, Delaive, Kel, Renard, Raes, Arnould: "Mild mitochondrial uncoupling does not affect mitochondrial biogenesis but downregulates pyruvate carboxylase in adipocytes: role for triglyceride content reduction." in: American journal of physiology. Endocrinology and metabolism, Vol. 302, Issue 9, pp. E1123-41, (2012) (PubMed).

Yoon, Kang, Ryu, Poo: "Identification of tyrosine-nitrated proteins in HT22 hippocampal cells during glutamate-induced oxidative stress." in: Cell proliferation, Vol. 43, Issue 6, pp. 584-93, (2010) (PubMed).

Gobin-Limballe, Djouadi, Aubey, Olpin, Andresen, Yamaguchi, Mandel, Fukao, Ruiter, Wanders, McAndrew, Kim, Bastin: "Genetic basis for correction of very-long-chain acyl-coenzyme A dehydrogenase deficiency by bezafibrate in patient fibroblasts: toward a genotype-based therapy." in: American journal of human genetics, Vol. 81, Issue 6, pp. 1133-43, (2007) (PubMed).

Aliases for ACADVL 抗体

acyl-CoA dehydrogenase very long chain (ACADVL) 抗体
acyl-Coenzyme A dehydrogenase, very long chain (Acadvl) 抗体
acyl-CoA dehydrogenase, very long chain (Acadvl) 抗体
acyl-CoA dehydrogenase very long chain (acadvl) 抗体
acyl-CoA dehydrogenase very long chain (Acadvl) 抗体
ACAD6 抗体
fb52d04 抗体
LCACD 抗体
VLCAD 抗体
vlcad 抗体
wu:fb52d04 抗体
wu:fc75e01 抗体
zgc:64067 抗体
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