电话:
+86 (0512) 65829739
传真:
+86 (010) 6788 5057
电子邮件:
orders@antibodies-online.cn

ACADVL 抗体

(Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL))
The protein encoded by this gene is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. This acyl-Coenzyme A dehydrogenase is specific to long-chain and very-long-chain fatty acids. A deficiency in this gene product reduces myocardial fatty acid beta-oxidation and is associated with cardiomyopathy. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Jul 2008].

48 results

ACADVL 适用: 人 WB, ELISA, IHC (p) 宿主: 小鼠 Monoclonal 5D3 unconjugated
Pubmed 2 references
产品编号 ABIN559746
 
ACADVL 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7175433
 
ACADVL 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN559745
 
ACADVL 适用: 人, 大鼠, 小鼠 WB, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6259716
 
ACADVL 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6136403
 
Verified ACADVL 适用: 人 WB, ELISA 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN571126
 
Verified ACADVL 适用: 人 WB, ELISA 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN1589990
 
ACADVL 适用: 人, 大鼠, Cow, 犬, 马, 兔, 斑马鱼, Pig, Hamster WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6738948
 
ACADVL 适用: 人, Cow, 犬, 马, 兔, 斑马鱼, Bat WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6745461
 
ACADVL 适用: 人, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN630886
 
ACADVL 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN928726
 
ACADVL 适用: 人, 大鼠, 小鼠, Cow, 犬, 马, 兔, 斑马鱼, 豚鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2785736
 
ACADVL 适用: 人, 大鼠, 小鼠, Cow, 犬, 马, 兔, 斑马鱼, 豚鼠, Pig WB, IHC 宿主: 兔 Polyclonal unconjugated
Pubmed 1 reference
产品编号 ABIN2785735
 
ACADVL 适用: 人 ELISA, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN708446
 
ACADVL 适用: 人 ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN708448
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN4995928
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN4995927
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN2809385
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN881024
 
ACADVL 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN881023
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (IHC)
    • Immunofluorescence (IF)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunoprecipitation (IP)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Flow Cytometry (FACS)
  • 适用
    • Human
    • Rat
    • Mouse
    • Cow
    • Dog
    • Horse
    • Rabbit
    • Zebrafish (Danio rerio)
    • Guinea Pig
    • Pig
    • Bat
    • Hamster
  • 论文引用
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Goat
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 32A31
    • 5D3
  • 抗原表位
    • AA 251-350
    • AA 403-497
    • C-Term
    • N-Term
    • AA 345-434
    • AA 538-576
    • AA 1-140
    • AA 38-87
    • AA 408-655
    • AA 471-520
    • AA 551-600
    • Internal Region
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • HRP
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • IgG2b
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • Verified
    • KO Validated
  • Supplier
    • antibodies-online
    • Signalway
    • Aviva Systems Biology
    • Biomatik
    • Boster Bio
    • Abbexa
    • NSJ Bioreagents
    • Wuhan Fine biotech

Latest Publications for our ACADVL 抗体

Nouws, Te Brinke, Nijtmans, Houten: "ACAD9, a complex I assembly factor with a moonlighting function in fatty acid oxidation deficiencies." in: Human molecular genetics, Vol. 23, Issue 5, pp. 1311-9, (2014) (PubMed).

De Pauw, Demine, Tejerina, Dieu, Delaive, Kel, Renard, Raes, Arnould: "Mild mitochondrial uncoupling does not affect mitochondrial biogenesis but downregulates pyruvate carboxylase in adipocytes: role for triglyceride content reduction." in: American journal of physiology. Endocrinology and metabolism, Vol. 302, Issue 9, pp. E1123-41, (2012) (PubMed).

Yoon, Kang, Ryu, Poo: "Identification of tyrosine-nitrated proteins in HT22 hippocampal cells during glutamate-induced oxidative stress." in: Cell proliferation, Vol. 43, Issue 6, pp. 584-93, (2010) (PubMed).

Gobin-Limballe, Djouadi, Aubey, Olpin, Andresen, Yamaguchi, Mandel, Fukao, Ruiter, Wanders, McAndrew, Kim, Bastin: "Genetic basis for correction of very-long-chain acyl-coenzyme A dehydrogenase deficiency by bezafibrate in patient fibroblasts: toward a genotype-based therapy." in: American journal of human genetics, Vol. 81, Issue 6, pp. 1133-43, (2007) (PubMed).

Aliases for ACADVL 抗体

acyl-CoA dehydrogenase very long chain (ACADVL) 抗体
acyl-Coenzyme A dehydrogenase, very long chain (Acadvl) 抗体
acyl-CoA dehydrogenase, very long chain (Acadvl) 抗体
acyl-CoA dehydrogenase very long chain (acadvl) 抗体
acyl-CoA dehydrogenase very long chain (Acadvl) 抗体
ACAD6 抗体
fb52d04 抗体
LCACD 抗体
VLCAD 抗体
vlcad 抗体
wu:fb52d04 抗体
wu:fc75e01 抗体
zgc:64067 抗体
You are here:
Chat with us!