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AASS 抗体

(Aminoadipate Semialdehyde Synthase (AASS))
This gene encodes a bifunctional enzyme that catalyzes the first two steps in the mammalian lysine degradation pathway. The N-terminal and the C-terminal portions of this enzyme contain lysine-ketoglutarate reductase and saccharopine dehydrogenase activity, respectively, resulting in the conversion of lysine to alpha-aminoadipic semialdehyde. Mutations in this gene are associated with familial hyperlysinemia. [provided by RefSeq, Jul 2008].

26 results

AASS 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC, ICC, FACS, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7601519
 
AASS 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7611055
 
AASS 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7611056
 
AASS 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7610280
 
AASS 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2193462
 
AASS 适用: 人 WB, ELISA, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2193463
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunocytochemistry (ICC)
    • Flow Cytometry (FACS)
    • Immunoprecipitation (IP)
    • Immunofluorescence (IF)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Enzyme Immunoassay (EIA)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Dog
    • Guinea Pig
    • Horse
    • Rabbit
    • Pig
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
  • 克隆形成能力
    • Polyclonal
  • 克隆
    • RB14893
    • RB14895
  • 抗原表位
    • AA 224-364
    • C-Term
    • AA 33-455
    • AA 477-926
    • AA 805-834
    • AA 812-841
    • Internal Region
    • AA 220-300
    • AA 243-292
    • AA 251-300
    • AA 264-294
    • AA 268-317
    • AA 272-301
    • AA 37-865
    • AA 878-926
    • Center
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • HRP
  • 抗体亚型
    • IgG
    • Ig Fraction
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Biomatik
    • Abcepta
    • USBio
    • Acris
    • Assay Biotechnology Company, Inc.
    • Aviva Systems Biology
    • Boster Bio
    • Cloud-Clone
    • Enogene Biotech

Latest Publications for our AASS 抗体

Houten, Te Brinke, Denis, Ruiter, Knegt, de Klerk, Augoustides-Savvopoulou, Häberle, Baumgartner, Coşkun, Zschocke, Sass, Poll-The, Wanders, Duran: "Genetic basis of hyperlysinemia." in: Orphanet journal of rare diseases, Vol. 8, pp. 57, (2013) (PubMed).

Aliases for AASS 抗体

aminoadipate-semialdehyde synthase (AASS) 抗体
aminoadipate-semialdehyde synthase (Aass) 抗体
LKR 抗体
LKR/SDH 抗体
LKRSDH 抗体
LOR 抗体
LOR/SDH 抗体
LORSDH 抗体
Lorsdh 抗体
SDH 抗体
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