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Exostosin 1 产品

(Exostosin 1 (EXT1))

Categories

This gene encodes an endoplasmic reticulum-resident type II transmembrane glycosyltransferase involved in the chain elongation step of heparan sulfate biosynthesis. Mutations in this gene cause the type I form of multiple exostoses. [provided by RefSeq, Jul 2008].

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Featured Exostosin 1 Categories

Exostosin 1 抗体

High quality antibodies with extensive validation data.

Exostosin 1 ELISA试剂盒

Reliable ELISA kits for a wide range of species.

Exostosin 1 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended Exostosin 1 抗体

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Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IF
Validations
  • (6)
Cat. No. ABIN3022737
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IF
Validations
  • (1)
  • (3)
Cat. No. ABIN515425
Quantity 100 μg
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, ELISA, IHC
Validations
  • (3)
Cat. No. ABIN6261628
Quantity 100 μL
Datasheet Datasheet

Recommended Exostosin 1 ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
  • (1)
Cat. No. ABIN6955674
Quantity 96 tests
Datasheet Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6966617
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method
Validations
Cat. No. ABIN1132682
Quantity 96 tests
Datasheet Datasheet

Recommended Exostosin 1 蛋白

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Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1353260
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1778297
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Tobacco (Nicotiana tabacum)
Validations
  • (1)
Cat. No. ABIN3115069
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our Exostosin 1 Products

Khoontawad, Hongsrichan, Chamgramol, Pinlaor, Wongkham, Yongvanit, Pairojkul, Khuntikeo, Roytrakul, Boonmars, Pinlaor: "Increase of exostosin 1 in plasma as a potential biomarker for opisthorchiasis-associated cholangiocarcinoma." in: Tumour biology, Vol. 35, Issue 2, pp. 1029-39, (2014) (PubMed).

Tian, Yan, Wen, Li, Li, Cai, Li, Du, Chen: "A splice mutation and mRNA decay of EXT2 provoke hereditary multiple exostoses." in: PLoS ONE, Vol. 9, Issue 4, pp. e94848, (2014) (PubMed).

Coulson-Thomas, Gesteira, Esko, Kao: "Heparan sulfate regulates hair follicle and sebaceous gland morphogenesis and homeostasis." in: The Journal of biological chemistry, Vol. 289, Issue 36, pp. 25211-26, (2014) (PubMed).

de Andrea, Reijnders, Kroon, de Jong, Hogendoorn, Szuhai, Bovée: "Secondary peripheral chondrosarcoma evolving from osteochondroma as a result of outgrowth of cells with functional EXT." in: Oncogene, Vol. 31, Issue 9, pp. 1095-104, (2012) (PubMed).

Synonyms and alternative names related to Exostosin 1

exostosin glycosyltransferase 1 (EXT1), exostoses (multiple) 1 (Ext1), exostosin glycosyltransferase 1b (ext1b), exostosin glycosyltransferase 1 (Ext1), exostosin like glycosyltransferase 1 (EXTL1), exostosin glycosyltransferase 1 S homeolog (ext1.S), exostosin glycosyltransferase 1a (ext1a), AA409028, EXT, fd07d06, LGCR, LGS, TRPS2, TTV, wu:fd07d06, xext1

Protein level used designations for Exostosin 1

  • Glucuronosyl-N-acetylglucosaminyl-proteoglycan 4-alpha-N- acetylglucosaminyltransferase
  • Langer-Giedion syndrome chromosome region
  • N-acetylglucosaminyl-proteoglycan 4-beta-glucuronosyltransferase
  • exostoses (multiple) 1
  • exostosin 1
  • exostosin-1
  • glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase
  • multiple exostoses protein 1
  • putative tumor suppressor protein EXT1
  • multiple exostoses protein 1 homolog
  • exostosin-1b
  • glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase 1b
  • multiple exostoses protein 1 homolog b
  • Glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase
  • Multiple exostoses protein 1 homolog
  • exostoses-like 1
  • Heparan sulfate copolymerase
  • N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase 1a
  • exostosin-1a
  • glucuronosyl-N-acetylglucosaminyl-proteoglycan
  • glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase 1a
  • multiple exostoses protein 1 homolog a
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