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COX6B1 抗体 (AA 1-86) (HRP)

COX6B1 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7149182
发货至: 中国
  • 抗原 See all COX6B1 抗体
    COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))
    抗原表位
    • 15
    • 11
    • 8
    • 8
    • 6
    • 2
    • 2
    • 2
    • 1
    • 1
    AA 1-86
    适用
    • 55
    • 7
    • 6
    • 6
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    宿主
    • 49
    • 6
    克隆类型
    • 51
    • 4
    多克隆
    标记
    • 25
    • 6
    • 5
    • 4
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This COX6B1 antibody is conjugated to HRP
    应用范围
    • 36
    • 28
    • 23
    • 13
    • 13
    • 12
    • 6
    • 3
    • 2
    • 1
    • 1
    ELISA
    交叉反应
    纯化方法
    >95%, Protein G purified
    免疫原
    Recombinant Human Cytochrome c oxidase subunit 6B1 protein (1-86AA)
    亚型
    IgG
    Top Product
    Discover our top product COX6B1 Primary Antibody
  • 应用备注
    Optimal working dilution should be determined by the investigator.
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    Preservative: 0.03 % Proclin 300
    Constituents: 50 % Glycerol, 0.01M PBS, PH 7.4
    储存液
    ProClin
    注意事项
    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C,-80 °C
    储存方法
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 抗原
    COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))
    别名
    COX6B1 (COX6B1 产品)
    别名
    COX6B antibody, COXG antibody, COXVIb1 antibody, cox6b antibody, cox6b1 antibody, cox6b1a antibody, coxg antibody, coxvib1 antibody, 2010000G05Rik antibody, Cox6b antibody, RGD1565270 antibody, Cox6b1 antibody, fa92g05 antibody, si:dkey-161j23.2 antibody, wu:fa92g05 antibody, zgc:92631 antibody, COX VIb-1 antibody, COX6B1 antibody, cytochrome c oxidase subunit Vib polypeptide 1 (ubiquitous) antibody, cytochrome c oxidase subunit 6B1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) L homeolog antibody, cytochrome c oxidase, subunit VIb polypeptide 1 antibody, cytochrome c oxidase subunit 6B antibody, cytochrome c oxidase subunit VIb polypeptide 1, pseudogene 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, COX6B protein antibody, cytochrome c oxidase subunit VIb polypeptide 1 antibody, COX6B1 antibody, cox6b1.L antibody, Cox6b1 antibody, Cox6b1-ps1 antibody, LOC100464665 antibody, COX6B antibody, cox6b1 antibody, LOC102143756 antibody
    背景

    Background: Defects in COX6B1 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110], also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.

    Aliases: COX 6B antibody, COX VIb 1 antibody, COX VIb-1 antibody, COX6B antibody, COX6B1 antibody, COXG antibody, COXVIb1 antibody, CX6B1_HUMAN antibody, Cytochrome c oxidase subunit 6B1 antibody, Cytochrome c oxidase subunit VIb antibody, Cytochrome c oxidase subunit VIb isoform 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, Cytochrome c oxidase subunit Vib polypeptide 1 antibody

    UniProt
    P14854
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